Pediatric Cardiology

, Volume 14, Issue 4, pp 223–226 | Cite as

Atypical presentation of Kawasaki disease in an infant

  • Andreas Gamillscheg
  • Gefried Zobel
  • Eva Felicitas Karpf
  • Drago Dacar
  • Albrecht Beitzke
  • Jörg Ingolf Stein
  • Christa Suppan
Case Reports


A 7-month-old male infant with clinical symptoms of severe toxic shock syndrome died on day 9 of illness. At autopsy, demonstration of coronary vasculitis together with thrombosis of the left coronary artery revealed the true diagnosis of atypical Kawasaki disease. The marked similarity in many clinical features makes the distinction between these two diseases difficult when atypical clinical presentation of Kawasaki disease is present.

Key Words

Atypical Kawasaki disease Toxic shock syndrome Infancy 


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Copyright information

© Springer-Verlag New York Inc. 1993

Authors and Affiliations

  • Andreas Gamillscheg
    • 1
  • Gefried Zobel
    • 2
  • Eva Felicitas Karpf
    • 4
  • Drago Dacar
    • 3
  • Albrecht Beitzke
    • 1
  • Jörg Ingolf Stein
    • 1
  • Christa Suppan
    • 1
  1. 1.Department of Pediatric CardiologyUniversity of GrazGrazAustria
  2. 2.Department of PediatricUniversity of GrazGrazAustria
  3. 3.Department of Cardiac SurgeryUniversity of GrazGrazAustria
  4. 4.Institute of PathologyUniversity of GrazGrazAustria

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