Acta Neuropathologica

, Volume 52, Issue 2, pp 165–167 | Cite as

Neuronal ceroid-lipofuscinosis and metachromasia

  • Martti Hormia
Short Original Communications

Summary

Two cases of neuronal ceroid-lipofuscinosis are described. They presented in the white matter granular material which stained metachromatically with toluidine blue in paraffin sections. The origin of this material is discussed.

Key words

Neuronal ceroid-lipofuscinosis Amaurotic idiocy Alcohol-resistant metachromasia Metachromatic leukodystrophy Cerebroside sulphatides 

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Copyright information

© Springer-Verlag 1980

Authors and Affiliations

  • Martti Hormia
    • 1
  1. 1.Department of PathologyCentral Hospital of North KareliaJoensuuFinland

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