Epidermolysis bullosa hereditaria dystrophica dominant with extensive skin defect at birth
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Summary
We report a case of epidermolysis bullosa hereditaria dystrophica dominant with an extensive skin defect on the left lower extremity present at birth. This case is of interest in that the scar contracture and the growth retardation of the affected extremity were present at birth. A full-thickness skin graft including the subdermal vascular network was applied to the contracted foot under general anesthesia at the age of 2 months. The graft and the donor site healed uneventfully. Now, the child is 3 years and 9 months old and no scar contracture has recurred. The function of the foot is normal.
Key words
Epidermolysis bullosa Congenital skin defect Inhibition of growth ContracturePreview
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References
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