Archives of oto-rhino-laryngology

, Volume 212, Issue 1, pp 1–14 | Cite as

Hereditary deafness in the Dalmatian dog

  • I. W. S. Mair


The temporal bones from 18 deaf Dalmatian dogs were examined with the light microscope, and the cochleo-saccular degeneration process studied. End organ degeneration is already advanced by the age of 4 weeks, whilst loss of neurons in the spiral ganglion was found only in adult animals. Both processes are first evident in the central portion of the cochlea, and increase in extent with advancing age. The implications of these findings for the management of non-conductive hearing loss in man are discussed.

Key words

Hereditary deafness Dalmatian dogs Cochleo-saccular degeneration Spiral ganglion degeneration 


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Copyright information

© Springer-Verlag 1976

Authors and Affiliations

  • I. W. S. Mair
    • 1
  1. 1.Department of OtolaryngologyUniversity of TromsøTromsøNorway

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