Gorham massive osteolysis
- 69 Downloads
Gorham syndrome (massive osteolysis) is a very rare tumour-like lesion characterized by progressive osteolysis. The diagnosis must be confirmed by the microscopic finding of intramedullary angioma-like vascular structures. We report a case of a 15-year-old boy with a pathological fracture in his left humerus. Imaging modalities such as magnetic resonance imaging, computed tomography, angiography and bone scintigraphy failed to disclose to tumorous lesion that filled a cavity in the left humerus. After observing the boy's progress for 6 months, a temporary diagnosis of Gorham syndrome was made, and surgical treatment was chosen. After resection of the left humeral head and the proximal one-quarter of the humerus, thorough curettage was performed in the distal humerus and an intramedullary artificial humeral head fixed with adequate success. Pathological examination of the specimen revealed intramedullary haemangioma of the humerus.
KeywordsPublic Health Compute Tomography Magnetic Resonance Imaging Image Modality Pathological Examination
Unable to display preview. Download preview PDF.
- 2.Cannon SR (1986) Massive osteolysis: a review of seven cases. J Bone Joint Surg [Br] 68:24–28Google Scholar
- 4.Gorham LW, Stout AP (1955) Massive osteolysis (acute spontaneous absorption of bone, phantom bone, disappearing bone). J Bone Joint Surg [Am] 37:985–1004Google Scholar
- 9.Heyden G, Kindbloom LG, Nielsen JM (1977) Disappearing bone disease: a clinical and histological study. J Bone Joint Surg [Am] 59:57–61Google Scholar
- l0.Jackson JBS (1838) A boneless arm. Boston Med Surg J 18:368–369Google Scholar
- 13.Leriche R (1937) À propos des osteolyses d'origine indeterminée. Mem Acad Chir 63:419–421Google Scholar
- 15.Pirier H (1968) Massive osteolysis of the humerus treated by resection and prosthetic placement. J Bone Joint Surg [Br] 50:158–160Google Scholar
- 19.Torg JS, Steel HH (1969) Sequential roentgenographic changes occurring in massive osteolysis. J Bone Joint Surg [Am] 51:1649–1655Google Scholar