Skeletal Radiology

, Volume 16, Issue 3, pp 227–231 | Cite as

Evaluation of radiographic abnormalities of the hand in patients with the Mayer-Rokitansky-Küster-Hauser syndrome

  • E. H. Strübbe
  • C. J. P. Thijn
  • W. N. P. Willemsen
  • R. Lappöhn


Radiographs of the hand in a group of 40 patients with the Mayer-Rokitansky-Küster-Hauser (MRKH) syndrome were studied. Most of the patients had the following abnormalities: brachymesophalangy of digits 2–5 (22/39 patients), small distal phalanx of digit 1 (22/39 patients), long proximal phalanx of digits 3–4 (19/39 patients), and long metacarpals of digits 1–4 (20/39 patients). In addition, three patients had distinct radial dysplasia and abnormalities of the carpals.

Key words

Mayer-Rokitansky-Küster-Hauser syndrome Pattern profile analysis Radial hypoplasia Scaphoid hypoplasia 


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Copyright information

© International Skeletal Society 1987

Authors and Affiliations

  • E. H. Strübbe
    • 3
  • C. J. P. Thijn
    • 3
  • W. N. P. Willemsen
    • 1
  • R. Lappöhn
    • 2
  1. 1.Department of Obstetrics and Gynecology, St. Radboud HospitalUniversity of NijmegenNijmegenThe Netherlands
  2. 2.Department of Obstetrics and GynecologyUniversity HospitalGroningenThe Netherlands
  3. 3.Department of RadiologyUniversity HospitalGroningenThe Netherlands

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