European Journal of Epidemiology

, Volume 7, Issue 5, pp 466–468 | Cite as

Risk of Creutzfeldt-Jakob disease in relation to animal spongiform encephalopathies: A collaborative study in Europe

  • A. Hofman


This paper describes a study of the risk of Creutzfeldt-Jakob disease in various European countries. The objectives of the study are to investigate the frequency of Creutzfeldt-Jakob disease and other human spongiform encephalophaties in Europe in relation to animal spongiform encephalophaties, and to assess the risk of Creutzfeldt-Jakob disease in relation to genetic, occupational and nutritional factors. The study will consist of three parts: the establishment of registries of Creutzfeldt-Jakob disease on the basis of cases in the registries, and molecular genetic studies with material collected in the registries.

Key words

Creutzfeldt-Jakob disease Animal spongiform encephalopathy Bovine spongiform encephalopathy Risk factors Europe 


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Copyright information

© Gustav Fischer 1991

Authors and Affiliations

  • A. Hofman
    • 1
  1. 1.Department of EpidemioloGy and BiostatisticsErasmus University Medical SchoolDR RotterdamThe Netherlands

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