Introduction

Cytochromes c are heme proteins that are encoded by nearly all organisms and function in the context of electron transport chains for cellular respiration and photosynthesis. In bacteria, cytochromes c are critical for the ability of organisms to use different energy sources and thus to inhabit multiple environmental niches1,2. Cytochromes c require the covalent attachment of heme (i.e., cytochrome c biogenesis) to a conserved CysXxxXxxCysHis motif via covalent thioether bond formation between the cysteine thiol and heme vinyl groups for proper protein folding and function3,4,5. Cytochrome c biogenesis can be accomplished by three pathways: System I (CcmABCDEFGH, \(\alpha\),\(\gamma\) Proteobacteria; plant and protozoal mitochondria; Archaea), System II (CcsBA, Gram (+); cyanobacteria; chloroplasts; \(\varepsilon\) Proteobacteria) and System III (HCCS, eukaryotic mitochondria) (reviewed in refs. 6,7,8,9,10,11,12,13). These three pathways use different mechanisms to interact with and position heme for attachment to the CXXCH motif. In bacteria, the cytochrome c biogenesis pathways also function to transport heme from the cytoplasmic site of synthesis, across the inner membrane to the site of attachment to apocytochrome c in the periplasm9,11,14.

Here we focus on System II, a bifunctional heme transporter and cytochrome c synthase5,15,16,17 (Fig. 1) composed of two integral membrane proteins termed CcsBA (also called ResBC)18,19,20,21,22,23,24,25,26. CcsBA has conserved features that are critical for its function. These include four conserved histidines that function as axial ligands to heme5,15, a tryptophan-rich WWD domain which stereospecifically positions heme for attachment to apocytochrome c15,16 and two large periplasmic domains16. The roles for these conserved features were determined by extensive biochemical and structure-function analyses5,15, as well as cryo-EM structural determination of the Helicobacter hepaticus CcsBA16. These studies revealed that CcsBA has two heme interaction domains. The transmembrane-heme (TM-heme) domain, consisting of two conserved histidines (TM-His1, TM-His2) and the periplasmic WWD/P-His domain composed of the WWD domain and two conserved histidines located in the periplasm (P-His1, P-His2)5,15,16. More recently, a computational study used RoseTTAFold27 to evaluate the predicted structures of CcsBAs from eight organisms and suggested that the function of the four conserved histidines and the interaction between the WWD domain and heme is highly conserved17. However, experimental confirmation of functional conservation predicted by computational studies has not yet been accomplished.

Fig. 1: Schematic of System II.
figure 1

System II, CcsBA (blue), is a bifunctional enzyme, which is proposed to transport heme (red) across the bacterial membrane and attach it to cytochrome c (yellow) at a conserved CXXCH motif. CcsBA is encoded as a single ORF that undergoes “natural proteolysis” resulting in CcsB and CcsA components5 as shown.

To date, most biochemical characterization of System II has relied on recombinantly expressed H. hepaticus CcsBA, the first CcsBA to be recombinantly expressed and affinity purified5. Recombinant studies are required as CcsBA is essential in many organisms18,19,24,25,28,29,30,31. System II is most commonly encoded as two proteins (CcsB CcsA), but examples exist where it is encoded as single-fused ORF (CcsBA)5,9. System II has presented technical challenges for recombinant expression. The single-fused ORF CcsBA has been amenable to recombinant studies and is stable and functional in E. coli5,32. In contrast, recombinant expression of System II encoded as two separate proteins (CcsB CcsA) in E. coli has not resulted in a functional CcsBA complex (e.g., ref. 33), limiting the ability to perform structure-function analyses. H. hepaticus CcsBA has proven to be an excellent model for characterization of CcsBA, however the lack of experimental data for CcsBAs from other organisms has been a major gap in the field.

Here, we describe the recombinant expression, affinity purification and structure-function analysis of CcsBAs from Helicobacter pylori and Campylobacter jejuni. H. pylori is a microaerophilic, Gram-negative bacteria, that is a common cause of chronic gastritis and is considered a causal factor for gastric ulcers and gastric cancer34. C. jejuni is a microaerophilic Gram-negative bacteria that commonly colonizes bird species and is a leading cause of human bacterial enteritis, which is often acquired through consumption of undercooked chicken35,36. The electron transport chains and the ability to switch between types of metabolisms has been implicated in the pathogenesis of both H. pylori37 and C. jejuni38,39. Therefore, understanding how cytochromes c, a critical component of these electron transport chains, are synthesized is of high importance. H. pylori only encodes a cytochrome c oxidase for growth in the presence of oxygen and a ccsBA deletion could not be obtained28. While C. jejuni encodes a cytochrome c oxidase and cytochrome bd for growth in the presence of oxygen28, yet ccsBA deletions were still not obtained under microaerobic growth conditions31. Thus, demonstrating that ccsBA is an essential gene in both these organisms28,31. Therefore, recombinant expression is required for genetic studies that investigate the conservation of heme interaction mechanisms and their impact on synthase function. In this study, experimental evidence for conservation of heme interaction and attachment to apocytochrome c is demonstrated.

Results

Predicted topology and structure of H. pylori and C. jejuni CcsBA

The well-characterized H. hepaticus CcsBA (WP_041309336.1) has 49.5% sequence identity to the H. pylori CcsBA (WP_000793250.1) and 40.3% sequence identity to C. jejuni CcsBA (CAL35131.1) (Supplementary Fig. 1). Each CcsBA is encoded as a single-fused ORF (Fig. 2a), contains two conserved histidines located in the transmembrane domains (TM-His1, TM-His2), two conserved histidines located in the periplasmic space (P-His1, P-His2) and a WWD domain (Fig. 2b and Supplementary Fig. 1). For consistency the TM-His1, 2 and P-His1, 2 nomenclature defined for H. hepaticus CcsBA was utilized here, and designations were determined by homology to H. hepaticus (Supplementary Fig. 1 and Table 1).

Fig. 2: Comparison of bacterial CcsBAs.
figure 2

a Schematic of CcsBA proteins from H. hepaticus, H. pylori and C. jejuni. N-terminal GST tag is shown in gray. Arrow denotes approximate location of natural proteolysis site. Molecular weights of affinity purified protein polypeptides are shown. b Protein sequences of CcsBA WWD domains (H. hepaticus: WP_041309336.1, H. pylori: WP_000793250.1 C. jejuni: CAL35131.1) are shown with conserved region highlighted in red. Asterisks indicate residues shown to form a cysteine/heme crosslink (H. hepaticus15, H. pylori, C. jejuni this study). c Cryo-EM structure of H. hepaticus CcsBA (open, PDB 79SY16). Heme in red and indicated by arrow with heme interaction domains labeled. d AlphaFold 3 predicted structure of H. pylori CcsBA (using protein sequence (WP_000793250.1)), e AlphaFold 3 predicted structure of C. jejuni CcsBA (using protein sequence (CAL35131.1)). PD1 periplasmic domain 1, PD2 periplasmic domain 2, dashed line indicates location of the beta-cap domain, WWD domain in sand, N-term and C-term are indicated. f Superimposition of H. hepaticus cryo-EM structure (deep purple) and H. pylori predicted structure (deep teal), RMSD 1.842. g Superimposition of H. hepaticus cryo-EM structure (deep purple) and C. jejuni predicted structure (forest green), RMSD 1.202.

Table 1 Designation of conserved histidines

H. pylori and C. jejuni were not included in the recent computational analysis of CcsBA structures17, thus AlphaFold 3 AI structural predictions40 of H. pylori and C. jejuni CcsBA were generated (confidence of predicted structures based on pLDDT are shown in Supplementary Fig. 2a, c) and compared to the H. hepaticus cryo-EM structure16 (Fig. 2c–g). Note that the H. hepaticus cryo-EM structure identified two conformations designated as “open” and “closed”. The “open” conformation had heme in the TM-heme domain and in the WWD/P-His domain, while “closed” had heme only in the TM-heme domain16. The “open” conformation showed more structural similarity to the AlphaFold 3 predictions, thus was used for all comparisons. Based on these structural predications and TMHMM topology analysis41 H. pylori and C. jejuni CcsBA each contain 14 transmembrane domains and two periplasmic domains (PD1, PD2), similar to other CcsBAs17. Topology schematics for each protein are provided (Supplementary Fig. 2b, d). Recently, a region of the PD1 domain was designated as the “beta cap domain”17 (Fig. 2c–e, dashed line). While the exact role for the PD1 beta cap domain has not been determined, it was proposed to occlude the CcsBA active site when heme is not present17. Here, the beta cap region of PD1 in H. pylori and C. jejuni was identified by homology to the H. hepaticus beta cap region (Fig. 2c–e, dashed line, Supplementary Fig. 2). Superimposition of the H. hepaticus cryo-EM structure with the computationally predicated H. pylori CcsBA AlphaFold 3 structure indicates a high level of structural conservation (RMSD 1.842 for overlay of complete structures), including positioning of the 14 TM domains and the PD1 and PD2 domains (Fig. 2f). Superimposition of the computationally predicated C. jejuni CcsBA AlphaFold 3 structure with the H. hepaticus CcsBA cryo-EM structure indicates structural conservation in positioning of the 14 transmembrane domains (RMSD 1.202 for overlay of complete structures), but structural differences in the PD1 domain. C. jejuni PD1 is predicted to have an additional beta-sheet region that extends above a structurally well-conserved beta sheet region (Fig. 2g). This beta-sheet extension region was predicted with 70–90% confidence by AlphaFold 3 (Supplementary Fig. 2c). C. jejuni CcsBA encodes more than 100 additional amino acids compared to H. hepaticus and H. pylori in the periplasmic domains (Supplementary Figs. 1 and 2), thus it is unsurprising that structural differences may exist, however direct evidence of these predicted differences awaits structural evidence. Despite the sequence and structural conservation of key features amongst CcsBAs it remains important to demonstrate experimentally that function is conserved.

Affinity purification of H. pylori and C. jejuni CcsBA

H. pylori CcsBA is 936 amino acids long with a predicted molecular weight of ~106 kDa. C. jejuni CcsBA has 1081 amino acids with a predicted molecular weight of ~123 kDa. An N-terminal GST fusion (~26 kDa) was engineered for each CcsBA (Fig. 2a). GST:CcsBAs were recombinantly expressed in E. coli C43 \(\Delta\)ccm (lacking the endogenous cytochrome c biogenesis genes) and affinity purified. Similar to H. hepaticus CcsBA, H. pylori (Fig. 3a, b lane 1) and C. jejuni (Fig. 3c, d lane 1) CcsBA affinity purifies as two major polypeptides (GST:CcsB’ and ‘CcsA). Note, C. jejuni CcsBA does exhibit additional degradation as indicated in the GST immunoblot (Fig. 3d, lane 1), however it is functional for synthase activity (Fig. 3e). The natural proteolysis of H. hepaticus CcsBA occurs at residue 368 and is located in a disordered region near TM5 in the cryo-EM structure5,16. Based on this data, the natural proteolysis sites for H. pylori and C. jejuni were predicted (Fig. 2a indicated by arrows, Supplementary Fig. 2) and the molecular weights for the proteolyzed fragments were calculated (Fig. 2a). As seen in other membrane proteins, specifically in other WWD domain containing proteins, a gel shift occurs resulting in the purified protein running faster than the predicted molecular weight. The proteolysis observed in recombinantly expressed H. pylori and C. jejuni CcsBAs provides experimental evidence that proteolysis is not limited to H. hepaticus CcsBA. Recent RoseTTAFold modeling of CcsBAs from eight other organisms suggests conservation of a disordered region near TM517, thus the observed natural proteolysis is unlikely to be an experimental artifact. In fact, a biological role for proteolysis is supported as multiple strategies to eliminate natural proteolysis were unsuccessful. For example, neither expression of H. hepaticus CcsBA in a panel of protease deficient E. coli strains nor a 20 amino acid deletion encompassing the site of natural proteolysis prevented the observed proteolysis15.

Fig. 3: Analysis of conserved histidines.
figure 3

The four conserved histidines in H. pylori and C. jejuni CcsBA were individually mutated to glycine. Proteins were affinity purified using an N-terminal GST tag, 5 µg were separated via 12.5% SDS-PAGE and visualized with (a, c) Coomassie total protein stain and (b, d) a GST specific antibody. Key molecular weight markers are indicated. CcsBA purifies as two major polypeptides: GST:CcsB’ and ‘CcsA. ‘—indicates natural proteolysis. GST*—proteolyzed GST. e, f The C. jejuni CcsBA His→Gly variants were co-expressed with cytochrome c4 in E. coli \(\triangle\)ccm. Synthase activity (i.e., heme attachment to cytochrome c4) was determined by separation of total cell lysate via SDS-PAGE and heme stain of holocytochrome c (24 kDa—full length; 12 kDa—endogenously proteolyzed). i, j Quantification of heme stained bands was performed with wildtype normalized to 100% synthase function. Three biological replicates, each containing three technical replicates were performed. A representative biological replicate is shown. g, h Chemical complementation of C. jejuni CcsBA His→Gly variants was performed as in (e), with supplementation of 10 mM imidazole. k, l Quantification of heme stained bands was performed as in (i) and a representative biological replicate is shown. Error bars show the standard deviation from the mean, dots indicate individual data points. WT wildtype, Vec vector control, * below limit of detection for heme stain.

Four conserved histidines are required for heme interaction and synthase function

To evaluate conservation of histidine function in CcsBA, the four conserved histidines of H. pylori and C. jejuni CcsBA were analyzed. Each of the conserved histidines (see Table 1) were mutated to glycine and an N-terminal GST tag was used for affinity purification. The histidine variants are stable (Fig. 3a–d). Analysis of heme co-purification for each variant was determined via UV-vis spectroscopy using the Soret peak (~412 nm). The H. pylori and C. jejuni CcsBA TM-His1Gly and TM-His2Gly variants co-purify with ~25% of the heme compared to wildtype (Supplementary Figs. 3a, b and 4a, b). The H. pylori P-His1Gly and P-His2Gly variants co-purify with ~50% of wildtype heme levels and C. jejuni P-His1Gly and P-His2Gly variants co-purify with approximately wildtype levels of heme (Supplementary Figs. 3a, b and 4a, b). Despite varying levels of heme co-purification, UV-vis spectroscopy analysis determined that the heme environment was otherwise similar to wildtype for the His→Gly variants (Supplementary Figs. 3c–g and 4c–g). These results are similar to the analysis of conserved histidines in H. hepaticus CcsBA5,15. This functional and heme co-purification data supports the model that TM-His1,2 are required for initial heme interaction with CcsBA and in their absence the CcsBA-heme interaction is greatly reduced. In contrast, mutation of P-His1,2 results in wildtype heme levels, suggesting heme is retained in the TM-heme domain as seen the H. hepaticus “closed” cryo-EM structure, leading to the model that heme is transferred from the TM-heme domain to the WWD/P-His domain16.

Previous results determined that the four conserved histidines (Supplementary Fig. 1) are required for CcsBA synthase function5,15,21,42,43. To determine if this role in synthase function is conserved for H. pylori and C. jejuni the TM-His1Gly, TM-His2Gly, P-His1Gly and P-His2Gly variants were recombinantly co-expressed with Bordetella pertussis cytochrome c4 in an E. coli strain lacking the endogenous cytochrome c biogenesis genes (E. coli \(\Delta\)ccm) and synthase function (i.e., heme attachment to cytochrome c) was monitored via an enhanced chemiluminescence (ECL)-based heme stain44. Note, this assay results in full-length holocytochrome c4 (24 kDa) and an endogenously proteolyzed 12 kDa fragment32. Under the experimental conditions, two independently constructed wildtype H. pylori CcsBA functional strains had an average of ~1/175 synthase function compared to H. hepaticus CcsBA (Supplementary Fig. 3h, i) therefore synthase function assays with H. pylori were not technically feasible as cytochrome c biogenesis levels were near the limit of detection for the heme stain. In C. jejuni CcsBA, the four conserved histidines were required for synthase function (Fig. 3e, f, i, j) providing further evidence that the conserved histidines are essential to CcsBA synthase function.

CcsBA TM-His1, 2 and P-His1 are axial ligands to heme

Histidines often function as axial ligands to heme. It was initially experimentally determined5 and confirmed by cryo-EM16 that the H. hepaticus CcsBA TM-His act as axial ligands to heme and compose the TM-heme site (alternatively called the cytoplasmic heme vestibule16,17). Recent structural predictions indicate that in the eight CcsBAs examined, TM-His1, 2 are positioned to act as axial ligands to heme17, as originally shown experimentally in H. hepaticus5. Here we experimentally determined that C. jejuni CcsBA TM-His1, 2 act as axial heme ligands utilizing chemical complementation with exogenous imidazole (Fig. 3g, h). Mutation of histidine to a smaller amino acid, such as alanine or glycine, results in a cavity. When exogenous imidazole is added the imidazole can enter the cavity, restore formation of the heme ligand, and thus protein function. This was originally demonstrated in whale-sperm myoglobin containing a His93Gly mutation and protein crystallization revealed imidazole in the His93Gly cavity bound to the heme iron45. Therefore, chemical complementation with imidazole provides evidence that a residue functions in axial liganding of heme. While alanine substitution is often used to biochemically determine the function of a residue, previous studies have demonstrated that alanine substitutions are not robustly chemically complemented with imidazole5,46, however glycine substitutions can be15, thus glycine substitutions were used in this study. The C. jejuni TM-His1, 2→Gly variants were recombinantly co-expressed with cytochrome c4 in E. coli \(\Delta\)ccm with 10 mM imidazole supplementation. C. jejuni CcsBA TM-His1Gly and TM-His2Gly are chemically complemented by imidazole (Fig. 3g, k) and therefore function as axial ligands to heme.

Next, the role of P-His1, 2 as axial ligands were assayed as described above. P-His1Gly was chemically complemented, while P-His2Gly was not (Fig. 3h, l). Similar to H. hepaticus the C. jejuni CcsBA P-His1Gly functions as an axial ligand to heme15. The role of P-His2 has not been defined, however lack of chemical complementation with imidazole was also observed in H. hepaticus CcsBA15. The P-His2 loop was poorly resolved in the H. hepaticus CcsBA cryo-EM structure16 and was poorly predicted in RoseTTAFold analyses17, suggesting P-His2 is located on a flexible loop. This structural evidence coupled with the lack of imidazole complementation of P-His2Gly15 (Fig. 3h, l) has led to the proposal that P-His2 undergoes initial ligand exchange with the apocytochrome c CXXCH motif histidine16,17. Of note, P-His2 in other cytochrome c biogenesis WWD domain containing proteins, CcmC47,48 and CcmF49, are also located on structurally flexible loops, suggesting this initial ligand exchange by P-His2 may be a common mechanism among these proteins.

Cysteine/heme crosslinking reveals conservation of heme interaction mechanism in the CcsBA WWD domain

CcsBA is a member of the heme-handling protein (HHP) family which also includes other cytochrome c biogenesis proteins CcmC and CcmF from System I50,51. This protein family contains a conserved, tryptophan-rich, heme-handling domain called the WWD domain50 (Supplementary Fig. 5). This domain has been shown to directly bind and stereospecifically position heme in all three HHP proteins15,16,52,53, thus is considered to be a key feature of the active sites of HHP family members. The CcsBA WWD domains have high sequence conservation (Fig. 2b), but the mechanism of heme interaction has only been experimentally determined in a single CcsBA15, thus it is essential to experimentally demonstrate if the residues required for heme interaction are conserved.

To identify residues involved with heme interaction in the H. pylori and C. jejuni CcsBA WWD domains, a cysteine/heme crosslinking approach was taken. Cysteine has a natural propensity to form a covalent bond with heme when the cysteine thiols and heme vinyl groups are in close proximity (Supplementary Fig. 6). Much like heme attachment to the apocytochrome c CXXCH motif, other cysteine residues can covalently trap or form a crosslink to heme when engineered into a putative heme interaction domain. The cysteine/heme crosslinking approach has been used to identify heme interacting residues in CcmC52 and CcmF53, as well as H. hepaticus CcsBA15. More recently, cryo-EM structures of CcmABCD47 and CcsBA16 confirmed these WWD-heme interactions, demonstrating the utility of cysteine/heme crosslinking to identify heme interaction domains.

The H. pylori CcsBA WWD domain is composed of eighteen residues (W827-W844). Single amino acid cysteine substitutions were engineered at each WWD residue in a GST:CcsBA fusion construct. Variants were recombinantly expressed, affinity purified and 5 μg of purified protein was separated via SDS-PAGE. All WWD cysteine variants were stable (Supplementary Fig. 7a, b). Formation of a cysteine/heme crosslink results in retention of heme at the ‘CcsA polypeptide, which encodes the WWD domain, while b-type or non-covalently bound heme is separated from the CcsBA polypeptides and runs with the dye front as “free” heme. To determine if a cysteine/heme crosslink was formed, the ratio of ‘CcsA:free heme was determined by quantification of a heme stain (Supplementary Fig. 7c). Note that “free” heme can transfer through the nitrocellulose membrane. To ensure accurate quantification of “free” heme, two nitrocellulose membranes are layered for protein transfers and both membranes are heme stained and quantified (see Supplementary Fig. 7f, g). Initially, cysteine variants with a ‘CcsA: “free” heme ratio of >2.0 (W827C, A828C, N829C, S831C, K841C, E842C, T843C) or residues that had been shown to form a cysteine/heme crosslink in H. hepaticus CcsBA15 (E830C, W836C, W838C) were further characterized. Subsequent analysis determined that H. pylori CcsBA WWD cysteine variants W827C, W836C and E842C form robust cysteine/heme crosslinks (Fig. 4a, b and Supplementary Fig. 7f, g) and are required for heme interaction in the WWD domain. H. pylori CcsBA affinity purified proteins have a degradation product that contains the WWD polypeptide as indicated by the heme-stained band (Fig. 4b *CcsA, Supplementary Fig. 7d–h). Note that covalently bound heme (i.e., from formation of a cysteine/heme crosslink) is retained at the protein polypeptide upon SDS-PAGE, therefore the heme-stained *CcsA band contains the WWD domain with crosslinked heme.

Fig. 4: The H. pylori WWD domain directly binds heme.
figure 4

Single amino acid cysteine substitutions were engineered at each residue in the H. pylori WWD domain. Each variant was recombinantly expressed in E. coli, affinity purified utilizing the N-terminal GST tag and analyzed for formation of a cysteine/heme crosslink via heme stain. The ratio of CcsA’ bound to b-type (free) heme was determined and variants with a ratio of >2.0 were selected for further analysis. Three cysteine variants form the cysteine/heme crosslink. Five µg of GST affinity purified protein was separated via SDS-PAGE and assayed for (a) protein stability and (b) formation of a cysteine heme crosslink. CcsBA purifies as two major polypeptides: GST:CcsB’ and ‘CcsA. ‘—indicates natural proteolysis. *CcsA—proteolyzed polypeptide containing the WWD domain with crosslinked heme. GST*—proteolyzed GST. Key molecular weight markers are indicated. cf UV-vis spectral analysis of 75 µg of affinity purified protein. As purified (black) and reduced (red) spectra with key peaks indicated are shown.

To determine if the cysteine variants disrupted the overall heme environment of H. pylori GST:CcsBA, UV-vis spectral analysis was performed. Cysteine substitution did not alter the overall heme environment (Fig. 4c–f). A caveat to these experiments is that UV-vis spectroscopy provides an average of the heme environment in a sample. It is known that CcsBA retains most of the heme in the cytoplasmic TM-heme site16, thus this b-heme is predicted to account for the majority of the heme signal. Therefore, even if the small amount of crosslinked heme in the WWD domain results in perturbation of the TM-heme environment, UV-vis spectra may not be sensitive enough to detect these changes.

The C. jejuni CcsBA WWD domain is composed of residues W974-W991 and similar to the analysis for H. pylori described above, 18 single amino acid substitutions were engineered in the GST:CcsBA WWD domain (W974C-W991C). All WWD cysteine variants were stable (Supplementary Fig. 8a, b) and were assessed for formation of the cysteine/heme crosslink (Supplementary Fig. 8c). As described above, residues that had a ‘CcsA:free heme ratio of >2.0 (W974C, E989C), or were homologous to H. hepaticus CcsBA cysteine/heme crosslinking residues (A975C, W983C, W985C, K988C), or had a visible heme stain band at the ‘CcsA polypeptide (N976C, E977C, S978C) were further studied. Subsequent purification and analysis of ‘CcsA:free heme ratio identified three cysteine variants that formed a cysteine/heme crosslink (W974C, W983C, E989C) (Fig. 5a, b and Supplementary Fig. 8d). Heme environments of these cysteine variants were similar to wildtype as determined by UV-vis spectroscopy (Fig. 5c–f). The C. jejuni cysteine/heme crosslinks at W974C and W983C exhibited a ‘CcsA:free heme ratio of >2.0, but were less robust than the crosslink formed by E989C. Overall C. jejuni CcsBA co-purified with lower heme amounts than H. pylori, which may account for the lower heme signal at ‘CcsA. Together, these analyses have identified conserved residues that are involved with heme binding and positioning in the WWD domain (Fig. 2b *s). Of note, this study identifies 3 WWD residues that are required for heme interaction across CcsBAs from three organisms, demonstrating that not only does the WWD have high sequence conservation, its mechanism for heme interaction is also highly conserved.

Fig. 5: The C. jejuni WWD domain directly binds heme and is required for synthase function.
figure 5

Single amino acid cysteine substitutions were engineered at each residue in the C. jejuni GST:CcsBA WWD domain. As described in the Figure, three variants were determined to form the cysteine/heme crosslink. Five µg of GST affinity purified protein was separated via 12.5% SDS-PAGE and assayed for (a) protein stability and (b) formation of cysteine heme crosslink. CcsBA purifies as two major polypeptides: GST:CcsB’ and ‘CcsA. ‘—indicates natural proteolysis. GST*—proteolyzed GST. Key molecular weight markers are indicated. cf UV-vis spectral analysis of 75 µg of affinity purified protein. As purified (black) and reduced (red) spectra with key peaks indicated are shown. g C. jejuni CcsBA WT or the WWD single amino acid cysteine variants were recombinantly expressed with cytochrome c4 in E. coli Δccm and synthase function was determined as described in Fig. 3e. Three biological replicates, each containing 3 technical replicates were performed. Representative samples are shown. h Quantitation of C. jejuni CcsBA WT and single amino acid cysteine variant synthase function as described in Fig. 3f. WT normalized to 100% synthase function. Error bars show the standard deviation from the mean, dots indicate individual data points. WT wildtype, Vec vector control, *below limit of detection for heme stain.

The CcsBA WWD domain is required for synthase function

The CcsBA WWD domain is required for synthase function5,15,42,43. To determine the role of individual C. jejuni WWD residues for synthase function, the WWD cysteine variants were co-expressed with cytochrome c4 in E. coli \(\Delta\)ccm and synthase function was determined as described above (Fig. 5g, h and Supplementary Fig. 9). Six residues (W974C, A975C, W979C, W985C, K988C, E989C) were essential for synthase function, defined as less than 5% synthase function compared to WT. Two residues (W983C, D986C) had severely reduced function, defined as 5-25% synthase function compared to wildtype. Three residues (R981C, S984C, W991C) had partial function, defined as 25-80% of wildtype synthase function. Seven residues (N976C, E977C, S978C, G980C, Y982C, S987C, T990C) had wildtype synthase function, defined as >80% of wildtype synthase function, thus are not required for C. jejuni CcsBA synthase function. While there are differences in the requirement of specific residues for synthase function across CcsBAs, this analysis identified three conserved residues that are required for synthase function across H. hepaticus and C. jejuni CcsBAs (C. jejuni: W974C, A975C, W979C; H. hepaticus: W828C, A829C, W833C15). Of note, a limited analysis of the Chlamydomonas reinhardtii CcsBA WWD domain was undertaken and residues homologous to C. jejuni W974 and W979 were also required for synthase function42. These results demonstrate that not only is the WWD domain required for synthase function and thus constitutes the active site of CcsBA, but we have also determined residues that contribute specifically to synthase function and heme binding.

Discussion

Here a comprehensive structure-function analysis of heme binding in H. pylori and C. jejuni CcsBAs was undertaken to determine if heme binding mechanisms are conserved in System II bacterial cytochrome c biogenesis. Previous work defined a TM-heme site on the cytoplasmic face of H. hepaticus CcsBA, composed of TM-His1 and TM-His25,15,16. We have experimentally shown that TM-His1,2 are required for heme binding in two additional CcsBAs, as His→Gly mutations drastically reduced heme co-purification (Supplementary Figs. 3a, b and 4a, b). Further, TM-His1,2 in C. jejuni CcsBA act as axial heme ligands (Fig. 3g, k). Experimental evidence that the H. pylori CcsBA TM-His1,2 are required for synthase function and act as axial heme ligands was not obtained due to low levels of synthase function (Supplementary Fig. 3h, i). However, based on conservation of TM-His1,2 and the experimental evidence from H. hepaticus CcsBA5,15, W. succinogenes CcsBAs43, Chlamydomonas reinhardtii21,42 and C. jejuni CcsBAs (Fig. 3e, g) we predict H. pylori TM-His1,2 will function as axial ligands to heme. Conservation of this TM-heme binding domain was predicted by computational analyses of eight CcsBAs17. AlphaFold 3 can predict protein-molecule interactions40 and was used to predict heme interaction with H. pylori and C. jejuni CcsBA. These structural predictions were compared with the H. hepaticus CcsBA cryo-EM and show positioning of TM-His1,2 is similar, supporting the chemical complementation data that these residues act as axial heme ligands (Fig. 6a–c).

Fig. 6: Heme binding mechanism is conserved in CcsBA.
figure 6

The cryo-EM structure of H. hepaticus CcsBA (deep purple, open, PDB 79SY16), AlphaFold 3 predicted structure of H. pylori CcsBA (deep teal) and AlphaFold 3 predicted structure of C. jejuni CcsBA (forest green) were used to examine heme binding in CcsBA. ac TM-His1 and TM-His2 (lime green) are positioned to act as axial ligands to heme localized in the TM-Heme site. Note, TM1 and TM2 are hidden for visualization of TM-His positioning. d The “WWD core”, consisting of the WWD domain and four surrounding transmembrane domains of each CcsBA were superimposed and 90° rotation is shown. TMs are labeled. eg The WWD domain is shown and residues that form a cysteine/heme crosslink are labeled and shown with amino acid structure.

Heme is proposed to be trafficked from the TM-heme site to the external WWD/P-His domain via a heme channel composed of the 4 TM domains (TM10, TM11, TM12, TM13) surrounding the WWD domain, termed the WWD domain “core region”. The structural architecture of the “core region” is conserved in H. hepaticus, H. pylori and C. jejuni CcsBAs (Fig. 6d), as well as other computationally predicted CcsBA structures17. Here we have experimentally shown that P-His1 and P-His2 of C. jejuni CcsBA are required for synthase function (Fig. 3f, j) and P-His1 is an axial ligand to heme (Fig. 3h, l). The WWD domain has now been shown to bind and stereospecifically position heme in three CcsBAs15 (Figs. 4b and 5b), as well as the other two members of the HHP family via cysteine/heme crosslinking52,53. This study demonstrates that the mechanism of heme binding within the WWD domain is highly conserved in CcsBAs and three residues of high importance were identified (Figs. 2b *s and 6e–g). Formation of the cysteine/heme crosslink confirms that these residues are in close proximity to the heme vinyl groups (Supplementary Fig. 10a, d–g). AlphaFold 340 predicted heme interaction with H. pylori and C. jejuni CcsBA WWD domains (Supplementary Fig. 10b, c) were compared to heme positioning in H. hepaticus CcsBA determined by cryo-EM (Supplementary Fig. 10). C. jejuni predicted heme positioning is similar to H. hepaticus with both heme vinyl groups located near a cysteine/heme crosslinking residue. H. pylori predicted heme positioning did not correspond to the H. hepaticus CcsBA heme positioning (Supplementary Fig. 10b), thus confirmation of heme vinyl group positioning in the WWD domains of H. pylori and C. jejuni CcsBA awaits structural determination. The cysteine/heme crosslinking results can also provide insight into positioning of the apocytochrome c CXXCH motif, which also must be close to heme vinyl groups for thioether bond formation. Computational studies predicted two binding pockets for the CXXCH motif in H. hepaticus CcsBA, called C1 (composed of the C-terminal WWD domain, specifically H. hepaticus residues D840, S841, K842, E843) and C2 (composed of N-terminal WWD domain, specifically H. hepaticus residues W828, A829, S832, W833)17. Of note, two of the three conserved cysteine/heme crosslinking residues determined here (homologous to H. hepaticus W828, E843), reside within those predicted CXXCH binding pockets. Utilizing the H. hepaticus cryo-EM structure with heme in the WWD domain W828C and E843C also have the shortest distance to the heme vinyl groups (Supplementary Fig. 10), thus it is unsurprising that cysteine substitutions at these residues form a cysteine/heme crosslink. Together this modeling and experimental evidence support that heme is positioned within the WWD domain to subsequently form thioether bonds to the CXXCH motif of apocytochrome c. In conclusion, this study demonstrates that heme interaction in the TM-heme, as well as positioning in the WWD/P-His domain of the bacterial cytochrome c synthase, CcsBA, is highly conserved.

The conservation of heme binding residues in the cytoplasmic TM-heme site and the periplasmic WWD/P-His heme domain determined here are important to our basic biological understanding of cytochrome c synthase function. Conservation of heme binding in the active site of CcsBA from multiple bacteria leads to the proposal that CcsBA could be a target for novel inhibitors. Early studies showed that addition of exogenous alternative metal porphyrins (e.g., ZnPPIX) inhibited cytochrome c biogenesis by recombinantly expressed System II and System I pathways54, demonstrating that inhibition of these pathways is feasible. CcsBA is an attractive target as it is essential in pathogens including H. pylori and C. jejuni18,19,24,25,28,29,30,31, thus targeting the synthase could inhibit pathogen growth. Additionally, differences in substrate recognition exist between CcsBA and the human cytochrome c synthase, HCCS, therefore cross-reactivity is unlikely. For example, in vivo studies suggested and recent in vitro reconstitution confirmed that HCCS requires the apocytochrome c CXXCH motif plus the preceding N-terminal alpha helix for substrate recognition55,56,57,58. In contrast, CcsBA has been shown to mature cytochromes c from various bacterial species, as well as the human cytochrome c59,60 and in vitro reconstitution demonstrated CcsBA heme attachment to a minimal 9-mer peptide (KCSQCHTVE)55. While there is a general need for novel therapeutics, H. pylori and Campylobacter species are designated as high-priority pathogens for new therapeutics due to their clarithromycin and fluroquinolone resistance, respectively61,62, thus novel antibiotic targets are of high importance. This study demonstrates conservation of WWD residues in heme binding (Figs. 4b and 5b) and synthase activity 5,15,42,43 (Fig. 5g, h) across CcsBAs. Therefore, we propose CcsBA, specifically the WWD domain is potentially an attractive target for novel therapeutics.

Methods

Bacterial growth conditions

Escherichia coli strains were grown in Luria-Bertani broth (LB; Difco) at 24 °C and 240 rpm for protein purifications or 37 °C and 200 rpm for functional assays with the following selective antibiotics and inducing reagents at the indicated concentrations: carbenicillin, 50 µg/ml; chloramphenicol, 20.4 µg/ml; isopropyl -D-1- thiogalactopyranoside (IPTG; Gold Biotechnology), 1.0 mM or 0.1 mM; L-arabinose (Gold Biotechnology), 0.2% (wt/vol).

Construction of strains and plasmids

All cloning was performed using E. coli NEB-5α. Construction of plasmids and generation of single amino acid substitutions is described in the Supplementary Methods. A complete list of strains, plasmids, and primers is provided in Supplementary Table 1.

CcsBA structural modeling

The H. pylori (strain ATCC 700392/26695) CcsBA and C. jejuni (strain ATCC 700819/NCTC 11168) CcsBA predicted structures were obtained using the AlphaFold 340 launched on 2024-05 to predict protein structures and protein-ligand (heme) interactions. For both the organisms, most of the predicted structures indicated a high level of model confidence (per residue confidence score, pLDDT, see Supplementary Fig. 2a, c). The PDB files of H. pylori & C. jejuni (obtained from AlphaFold 3 prediction) and H. hepaticus CcsBA open (PDB: 7S9Y16) conformation were uploaded to PyMOL (version 2.5.2). Then these structures were superimposed to give the root mean standard deviation (RMSD) values between them.

Protein purifications

E. coli strain C43 was used for protein expression and GST affinity purifications of GST:CcsBA were performed as previously described15. Details are provided in Supplementary Methods.

Heme staining, immunoblotting and quantification

Heme staining was performed as previously described utilizing an ultrasensitive, long duration ECL-based development (Thermo Scientific FEMTO kit)15,44,53. Immunoblots were performed using 5 μg of affinity purified proteins and α-GST (1:75000) (Invitrogen, PA1-982A), primary, protein A peroxidase (Millipore Sigma, P8651) as a secondary label and a standard ECL development. Imaging was performed on Sapphire Biomolecular Imager (Azure Biosystems) and quantified with imaging software (Azure Spot v.2.2.167).

UV-visible absorption spectroscopy

UV-visible absorption spectra were collected with a UV-1900i spec and LabSolutions software (Shimadzu; LabSolutions UV-vis version 1.10) as described in ref. 15. Briefly, 75 μg of affinity purified protein was used to collect spectra from 360–800 nm. Quantitation of total heme levels used the Soret region (~411–414 nm). Sodium hydrosulfite powder (Sigma 157-953) was used to reduce protein spectra. Note that initial CcsBA studies did not accomplish complete reduction of CcsBA5, subsequent studies determined that in order to obtain a completely reduced CcsBA spectra, excess sodium hydrosulfite is required15.

Functional (heme attachment) assays

The indicated CcsBA variants were co-expressed with cytochrome c4:His (pRGK332) in strain C43 Δccm::KanR. Heme staining was performed on all samples to confirm the heme attachment function of CcsBA variants as described previously15,32,63. Details are provided in the Supplementary Methods.

Statistics and reproducibility

Statistical analysis of data presented in graphs was performed in Microsoft Excel. All protein purifications were performed independently and a minimum of three times. All UV-vis spectral analysis was performed with independent protein preparations a minimum of two times. All functional experiments were performed independently and in triplicate with biological and/or technical replicates, as described in figure legends.

Reporting summary

Further information on research design is available in the Nature Portfolio Reporting Summary linked to this article.