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Spontaneously Ruptured Dural Ectasia in a Patient with Marfan Syndrome: a Case Report and Discussion of the Challenges Faced

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Abstract

Dural ectasia is a common finding in patients with Marfan syndrome, while many of these patients are on anticoagulants due to prosthetic heart valves. A 44-year-old man was transferred to the ER due to cauda equina syndrome. The patient was on warfarin. His CT scan revealed spontaneous hemorrhage in the lumbosacral region. The patient underwent an urgent laminectomy with subtotal removal of haemorrhagic tissue. Post-operatively, he developed sepsis due to wound leak. Additionally he developed resistance to heparin. The complications were successfully managed, and the patient was discharged 3 months after his admission. People with Marfan syndrome could have significant co-morbidities while their management can be complicated by various issues. We present a case of lumbosacral hemorrhage and cauda equina with the background of dural ectasia and anticoagulants and discuss the relevant set of complications and their management.

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Authors and Affiliations

  1. Department of Neurosurgery, Nicosia General Hospital, Old Nicosia Limassol Road 215, Postcode 2029, Nicosia, Cyprus

    Ifigeneia Gioti, Dimitrios Nikolaides, Constantinos Picolas & Konstantinos Faropoulos

Authors
  1. Ifigeneia Gioti
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  2. Dimitrios Nikolaides
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  3. Constantinos Picolas
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  4. Konstantinos Faropoulos
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Contributions

All authors contributed equally for this work. K. Faropoulos, MD, PhD, has the supervision and is the corresponding author.

Corresponding author

Correspondence to Konstantinos Faropoulos.

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The work is in accordance with the principles of Nicosia General Hospital, The Scientific Committee, Ethical Board. All procedures performed in studies involving human participants were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki declaration and its later amendments or comparable ethical standards.

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A retrospective permission was taken by the “Nicosia General Hospital, The Scientific Committee, Ethical Board.”

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A retrospective permission was taken by the “Nicosia General Hospital, The Scientific Committee, Ethical Board.”

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The authors declare no competing interests.

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Gioti, I., Nikolaides, D., Picolas, C. et al. Spontaneously Ruptured Dural Ectasia in a Patient with Marfan Syndrome: a Case Report and Discussion of the Challenges Faced. SN Compr. Clin. Med. 4, 8 (2022). https://doi.org/10.1007/s42399-021-01100-1

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  • DOI: https://doi.org/10.1007/s42399-021-01100-1

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