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Ganglioneuroma Presenting as Presacral Mass: Surgical Management of a Rare Tumor—A Case Report

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Abstract

Presacral ganglioneuroma is an extremely rare and benign tumor of neural crest origin. To the best of our knowledge, less than 30 cases have been reported in adult population. The goal of this case report is to draw the medical community attention to an unusual diagnosis and we emphasize clinical features, imagiological findings, and surgical management of this rare entity. We report a case of a presacral ganglioneuroma, 5.2 × 5.6 × 6.7 cm in size, which was found in a young woman with suprapubic pain and amenorrhea. Complete tumor resection was achieved using the Kraske technique. The patient had an uneventful recovery. Presacral tumors are rare in adults. A magnetic resonance imaging is the radiological investigation method of choice. Preoperative biopsy is controversial. Surgery is the primary means of diagnosis and treatment and is always recommended. Three approaches are described: abdominal, posterior (Kraske), and combined. The choice of technique depends on the size of the tumor, the location relative to S3, and the extent of adjacent structures. The prognosis is generally favorable.

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Authors and Affiliations

  1. General Surgery Department, Centro Hospitalar Vila Nova de Gaia/Espinho, Rua Conceição Fernandes, Vila Nova de Gaia, 4434-502, Porto, Portugal

    Bárbara N. Castro, Ana R. Ferreira, Tatiana M. Queirós, Hugo Louro, Sílvia Costa, Susana Graça, Bela Pereira, João Cardoso & Manuel Oliveira

  2. Department of Pathology, Centro Hospitalar Vila Nova de Gaia/Espinho, Porto, Portugal

    Maria Shekhovtsova

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  1. Bárbara N. Castro
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  2. Ana R. Ferreira
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  3. Tatiana M. Queirós
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  4. Maria Shekhovtsova
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  5. Hugo Louro
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  6. Sílvia Costa
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  7. Susana Graça
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  8. Bela Pereira
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  9. João Cardoso
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  10. Manuel Oliveira
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Contributions

Bárbara N. Castro wrote the article and all the other authors reviewed and performed the necessary amendments to its improvement. All authors proofread the final version and approved it for publication.

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Correspondence to Bárbara N. Castro.

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The manuscript is in accordance with the 1964 Helsinki Declaration and its later amendments or comparable ethical standards. This article does not contain any studies with human participants or animals performed by any of the authors.

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Castro, B.N., Ferreira, A.R., Queirós, T.M. et al. Ganglioneuroma Presenting as Presacral Mass: Surgical Management of a Rare Tumor—A Case Report. SN Compr. Clin. Med. 3, 1828–1837 (2021). https://doi.org/10.1007/s42399-021-00951-y

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  • DOI: https://doi.org/10.1007/s42399-021-00951-y

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