Abstract
Sex cord stromal tumour (SCST) of ovary account for 5–8% of all ovarian malignancies. These include fibroma, thecoma, fibro-thecoma, Leydig cell tumour, granulosa cell tumour, and Sertoli cell tumour. Although considered primary ovarian malignancy, SCST has been described in extraovarian location also. Extraovarian SCST is a rare occurrence, and so far, only 25 cases have been reported in literature and only one amongst them was extraovarian fibroma with minor sex cord element. Considering the rarity, diagnosis and proper treatment remain the real challenge in these tumours. To the best of our knowledge, this is the second case of extraovarian fibroma with minor sex cord element to be reported. Herein, we report a case of 41-year-old lady who presented with large abdomino-pelvic mass which was considered ovarian tumour; however, intraoperatively both ovaries and uterus were found to be normal, and the mass was actually arising from sigmoid mesocolon.
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Data Availability
Data is available with author and appropriate consent was obtained from patient.
Abbreviations
- SCST:
-
Sex cord stromal tumour
- CECT:
-
Contrast enhanced computerised tomography
- GIST:
-
Gastro intestinal stromal tumour
- WHO:
-
World Health Organisation
- HnE:
-
Haematoxylin and eosin
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Contributions
Monika Pohekar: data acquisition, primary manuscript drafting.
Sabireen: manuscript review and editing.
Sandip Bipte: revising the manuscript critically.
Rajesh S. Shinde: conception and design, finalisation of manuscript.
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Highlights
1. Extraovarian fibroma with minor sex cord elements is a rare entity and management guidelines are not clearly defined.
2. The pre-operative diagnosis by clinico-radiological findings is difficult to establish and hence poses a diagnostic dilemma.
3. The follow-up of patients opting for fertility-preserving surgery is crucial as the chances of developing endometrial carcinoma are high. The option of completion of surgery was discussed with our patient, and she chose close surveillance. The patient is doing well at 2-year follow-up.
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Pohekar, M., Sabireen, Bipte, S. et al. Extraovarian Fibroma with Minor Sex Cord Elements—a Rare Tumour at Rare Site. Indian J Surg Oncol (2024). https://doi.org/10.1007/s13193-024-01951-9
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DOI: https://doi.org/10.1007/s13193-024-01951-9