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A Rare Case of Acute on Chronic Intestinal Pseudo-Obstruction Secondary to Primary Visceral Myopathy

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Abstract

Chronic intestinal pseudo-obstruction (CIPO) is a rare disabling disorder characterized by a severe impairment of gastrointestinal motility, mimicking mechanical obstruction in the absence of any occluding lesion of the gut lumen. The clinical presentation of CIPO includes variable degrees of nausea, vomiting, abdominal pain and abdominal distension. Visceral myopathy is a rare chronic disease of the bowel presenting with intermittent pseudo-obstruction. We present a rare case of intestinal pseudo-obstruction secondary to visceral myopathy in a 62-year-old female who presented with acute intestinal obstruction and was managed surgically. This report emphasizes that visceral myopathy although rare should be considered in the differential diagnosis of cases presenting with acute on chronic intestinal pseudo-obstruction.

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Authors and Affiliations

  1. GI Surgery, Believers Church Medical College, Thiruvalla, Kerala, India

    Sujith Philip

  2. General Surgery, Believers Church Medical College, Thiruvalla, Kerala, India

    Mano Zac Mathews & Bobby Johns

  3. Department of Pathology, CMC Vellore, Tamil Nadu, Vellore, India

    Anna B. Pulimood

Authors
  1. Sujith Philip
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  2. Mano Zac Mathews
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  3. Anna B. Pulimood
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  4. Bobby Johns
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Contributions

Operative work: SP, MZM, BJ; conceptualization and manuscript writing: SP, MZM; repeated editing and reviewing: SP, MZM, ABP, BJ; histopathological diagnosis work up: ABP; extensive literature search: MZM, BJ.

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Correspondence to Mano Zac Mathews.

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The authors declare no competing interests.

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Philip, S., Mathews, M.Z., Pulimood, A.B. et al. A Rare Case of Acute on Chronic Intestinal Pseudo-Obstruction Secondary to Primary Visceral Myopathy. Indian J Surg 85, 638–642 (2023). https://doi.org/10.1007/s12262-022-03507-z

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  • DOI: https://doi.org/10.1007/s12262-022-03507-z

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