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Embryonal Rhabdomyosarcoma of the Oral Cavity

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Abstract

A 19 year old female presents to the emergency room with right facial enlargement. Clinical examination revealed a soft tissue mass of the right buccal mucosa. Treated initially as infection, the patient later turned to clinic with now rapidly enlarging and intermittently painful mass. Computed tomography with contrast showed a low attenuated buccal mass with mild enhancement lateral to the right caudal maxilla and superior mandible. Biopsy was performed and microscopic examination showed cells with moderate pleomorphism with numerous atypical mitotic figures and occasional elongated “strap” cells with eccentric nuclei. Fluorescence in situ hybridization analysis revealed no rearrangement of the FKHR gene. The diagnosis of embryonal rhabdomyosarcoma was rendered. The patient was referred to the local children’s hospital for definitive treatment.

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Authors and Affiliations

  1. Department of Anatomic Pathology, Naval Medical Center San Diego, 34800 Bob Wilson Drive, San Diego, CA, 92134-5000, USA

    Mark McInturff, Anne Adamson, Chadwick Donaldson & Brenda L. Nelson

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  1. Mark McInturff
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  2. Anne Adamson
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  3. Chadwick Donaldson
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  4. Brenda L. Nelson
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Correspondence to Mark McInturff.

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This article does not contain any studies with human participants or animals performed by any of the authors.

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Disclaimer: The opinions and assertions expressed herein are those of the author and are not to be construed as official or representing the views of the Department of the Navy or the Department of Defense.

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McInturff, M., Adamson, A., Donaldson, C. et al. Embryonal Rhabdomyosarcoma of the Oral Cavity. Head and Neck Pathol 11, 385–388 (2017). https://doi.org/10.1007/s12105-016-0761-2

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  • DOI: https://doi.org/10.1007/s12105-016-0761-2

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