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An Unusual Tumor in an Uncommon Site-Orbital Rosai–Dorfman Disease: A Case Report

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Indian Journal of Otolaryngology and Head & Neck Surgery Aims and scope Submit manuscript

Abstract

Rosai–Dorfman disease (RDD) is also known as Sinus Histiocytosis with Massive Lymphadenopathy. It is a rare, benign, self-limiting disease of phagocytic histiocytes presenting with massive painless cervical lymphadenopathy. RDD can present as a nodal disease and also extra-nodal involvement with episodes of exacerbation and remissions and relapses after treatment. Its etiology remains poorly understood and is highly variable in its clinical presentation and response to treatment. Its treatment is poorly defined but the prognosis is usually fair. Here we are reporting a rare, unusual clinical presentation of infraorbital soft tissue mass diagnosed as RDD with cyto-histopathological correlation. Only a few such cases have been reported in the literature.

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Author notes

  1. Akshat Kushwaha

    Present address: Department of Otorhinolaryngology, JIPMER, Puducherry, 605006, India

Authors and Affiliations

  1. Department of Otorhinolaryngology, JIPMER, Puducherry, 605006, India

    Rashmi Hansdah, Sunil Kumar Saxena & Arun Alexander

  2. Department of Pathology, JIPMER, Puducherry, 605006, India

    Sreerekha Jinkala

Authors
  1. Rashmi Hansdah
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  2. Akshat Kushwaha
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  3. Sunil Kumar Saxena
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  4. Sreerekha Jinkala
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  5. Arun Alexander
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Contributions

All authors contributed to the study's conception and design. Material preparation, data collection, and analysis were performed by RH and AK, SKS, SJ, and AA. The first draft of the manuscript was written by AK and all authors commented on previous versions of the manuscript. All authors read and approved the final manuscript.

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Correspondence to Akshat Kushwaha.

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Hansdah, R., Kushwaha, A., Saxena, S.K. et al. An Unusual Tumor in an Uncommon Site-Orbital Rosai–Dorfman Disease: A Case Report. Indian J Otolaryngol Head Neck Surg 74 (Suppl 3), 5584–5587 (2022). https://doi.org/10.1007/s12070-021-02908-y

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  • DOI: https://doi.org/10.1007/s12070-021-02908-y

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