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Cochlear Implant in Klippel-Feil Syndrome: Challenges and Concerns

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Abstract

Cochlear implantation (CI) can be safely performed in patients with syndromic hearing loss. Here we present a case of CI in a child with Klippel-Feil syndrome with various skeletal, extraskeletal, cochleovestibular and Arnold-Chiari malformations. Multidisciplinary approach and good preoperative imaging play a key role in planning for surgery.

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References

  1. Mahiroğullari M, Ozkan H, Yildirim N, Cilli F, Güdemez E (2006) Klippel-Feil syndrome and associated congenital abnormalities: evaluation of 23 cases. Acta Orthop Traumatol Turc 40(3):234–239

    Google Scholar 

  2. Tracy MR, Dormans JP, Kusumi K (2004) Klippel-Feil syndrome: clinical features and current understanding of etiology. Clin Orthop Relat Res 424:183–190

    Article  Google Scholar 

  3. McElveen JT Jr, Carrasco VN, Miyamoto RT, Linthicum FH Jr (1997) Cochlear implantation in common cavity malformations using a transmastoid labyrinthotomy approach. Laryngoscope 107(8):1032–1036. https://doi.org/10.1097/00005537-199708000-00005

    Article  Google Scholar 

  4. McGaughran JM, Kuna P, Das V (1998) Audiological abnormalities in the Klippel-Feil syndrome. Arch Dis Child 79(4):352–355. https://doi.org/10.1136/adc.79.4.352

    Article  CAS  Google Scholar 

  5. Archbold S, Lutman ME, Nikolopoulos T (1998) Categories of auditory performance: inter-user reliability. Br J Audiol 32(1):7–12. https://doi.org/10.3109/03005364000000045

    Article  CAS  Google Scholar 

  6. Nargozian C (2004) The airway in patients with craniofacial abnormalities. Paediatr Anaesth 14(1):53–59. https://doi.org/10.1046/j.1460-9592.2003.01200.x

    Article  Google Scholar 

  7. Sennaroglu L (2010) Cochlear implantation in inner ear malformations—a review article. Cochlear Implants Int 11(1):4–41. https://doi.org/10.1002/cii.416

    Article  Google Scholar 

  8. Tucci DL, Telian SA, Zimmerman-Phillips S, Zwolan TA, Kileny PR (1995) Cochlear implantation in patients with cochlear malformations. Arch Otolaryngol Head Neck Surg 121(8):833–838. https://doi.org/10.1001/archotol.1995.01890080005001

    Article  CAS  Google Scholar 

  9. O’Malley JT, Burgess BJ, Galler D, Nadol JB Jr (2017) Foreign body response to silicone in cochlear implant electrodes in the human. Otol Neurotol 38(7):970–977. https://doi.org/10.1097/MAO.0000000000001454

    Article  Google Scholar 

  10. Wang H, Chen P (2013) Surgicel® (oxidized regenerated cellulose) granuloma mimicking local recurrent gastrointestinal stromal tumor: a case report. Oncol Lett 5(5):1497–1500. https://doi.org/10.3892/ol.2013.1218H

    Article  Google Scholar 

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Acknowledgements

The authors would like to gratefully acknowledge and thank the faculty, patient and attendants for accepting for publication.

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The author(s) received no financial support for the research, authorship, and/or publication of this article.

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Authors and Affiliations

  1. Department of Otolaryngology, Otology, Neurotology and Cochlear Implant Unit, Christian Medical College, Vellore, Tamil Nadu, 632004, India

    Y. Mounika Reddy, Anjali Lepcha, Ann Mary Augustine & Ajay Philip

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  1. Y. Mounika Reddy
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  2. Anjali Lepcha
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  3. Ann Mary Augustine
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  4. Ajay Philip
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Correspondence to Y. Mounika Reddy.

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Reddy, Y.M., Lepcha, A., Augustine, A.M. et al. Cochlear Implant in Klippel-Feil Syndrome: Challenges and Concerns. Indian J Otolaryngol Head Neck Surg 74 (Suppl 3), 3901–3905 (2022). https://doi.org/10.1007/s12070-021-02728-0

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  • DOI: https://doi.org/10.1007/s12070-021-02728-0

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