Abstract
Inner ear malformations are an important cause of sensorineural hearing loss ranging from severe to profound and they also contribute to Cerebrospinal fluid leakage and recurrent meningitis. The most severe is the complete labyrinthine aplasia (Michel Deformity), then there is cochlear aplasia, cochlear hypoplasia, incomplete partition of the cochlea, enlarged vestibular acqueduct and cochlear aperture abnormality.
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References
Jackler RK, Luxford WM, House WF (1987) Congenital malformations of the inner ear: a classification based on embryogenesis. Laryngoscope 97(suppl 40):2–14
Phelps PD, King A, Michaels L (1994) Cochlear dysplasia and meningitis. Am J Otol 15:551–557
Sennaroglu L, Bajin MD (2017) Classification and current management of inner ear malformations. Balk Med J 34:397–411
Grover M, Sharma S, Preetam C et al (2019) J LaryngolOtol 133:368–375. https://doi.org/10.1017/S0022215119000884
Tyagi I, Syal R, Goyal A (2005) Cerebrospinal fluid otorhinorrhoea due to inner-ear malformations: clinical presentation and new perspectives in management. J Laryngol Otol 119(9):714–718
Sennaroglu L (2016) Histopathology of inner ear malformations: do we have enough evidence to explain pathophysiology? Cochlear Implant Int 17:3–20
Kontorinis G, Goetz F, Giourgas A et al (2012) Radiological diagnosis of incomplete partition type I versus type II: significance for cochlear implantation. Eurradiol 22:525–532
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Gupta, A.K., Grover, M., Samdani, S. et al. CSF Otorhinorrhea Due to Inner Ear Malformation-A Case Report. Indian J Otolaryngol Head Neck Surg 74 (Suppl 3), 3773–3775 (2022). https://doi.org/10.1007/s12070-021-02582-0
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DOI: https://doi.org/10.1007/s12070-021-02582-0