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Langerhans Cell Histiocytosis in Paediatric Zygoma Swelling

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Abstract

Langerhans cell histiocytosis (LCH) is a rare neoplasm characterized by accumulation of histiocytes in various tissues. It has a wide clinical spectrum and its presentation may mimic clinical features of common diseases. High level of suspicion is required for early diagnosis. Here is a rare case of a rapidly aggressive LCH which first presented with right zygomatic swelling.

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Authors and Affiliations

  1. Otorhinolaryngology Department, Hospital Sultanah Aminah, Jalan Persiaran Abu Bakar Sultan, 80100, Johor Bahru, Johor, Malaysia

    Syiao Wei Ng, Faredza Aliyaa Zakawi, Jothi Shanmuganathan & Syarifah Nafisah Al-Yahya

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  1. Syiao Wei Ng
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  2. Faredza Aliyaa Zakawi
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  3. Jothi Shanmuganathan
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  4. Syarifah Nafisah Al-Yahya
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Correspondence to Syiao Wei Ng.

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Ng, S.W., Zakawi, F.A., Shanmuganathan, J. et al. Langerhans Cell Histiocytosis in Paediatric Zygoma Swelling. Indian J Otolaryngol Head Neck Surg 74 (Suppl 3), 5905–5909 (2022). https://doi.org/10.1007/s12070-021-02480-5

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  • DOI: https://doi.org/10.1007/s12070-021-02480-5

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