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Igg4 Related Disease of Skull Base—A Diagnostic Challenge

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Indian Journal of Otolaryngology and Head & Neck Surgery Aims and scope Submit manuscript

Abstract

IgG4 related disease (IgG4-RD) is a fibro-inflammatory disease, with tendency to affect any organ of the body. However, few cases affecting the skull base have been reported in literature. We report one such case in an elderly male, who presented us with a mass lesion in the skull base that mimicked nasopharyngeal malignancy. On thorough clinical history, examination, and investigations, IgG4 Related disease was diagnosed and treatment was started for it. The patient responded well to the treatment and is on follow up.

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Authors and Affiliations

  1. Department of ENT-HNS, Apollo Hospitals, Bangalore, 560076, Karnataka, India

    Krishna Ramanathan, Satish Nair & V. Pavithra

  2. Department of Interventional Radiology and Neuroradiology, Apollo Hospitals, Bangalore, Karnataka, India

    Savith Kumar

  3. Department of Neurology, Apollo Hospitals, Bangalore, Karnataka, India

    Gurucharan Adoor

  4. Department of Rheumatology, Apollo Hospitals, Bangalore, Karnataka, India

    Uma Karjigi

  5. Department of Pathology, Apollo Hospitals, Bangalore, Karnataka, India

    Swarna Shivakumar

Authors
  1. Krishna Ramanathan
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  2. Satish Nair
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  3. V. Pavithra
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  4. Savith Kumar
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  5. Gurucharan Adoor
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  6. Uma Karjigi
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  7. Swarna Shivakumar
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Contributions

SN: Substantial contributions to the conception or design of the work, revising it critically for important intellectual content, analysis and interpretation of data for the work and drafting the work and final approval of the version to be published.

KR, PV, SK, GA, UK, SS: Revising the content critically for important intellectual content and final approval of the version to be published.

KR: Substantial contributions to the acquisition of data for the work.

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Correspondence to Krishna Ramanathan.

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Ramanathan, K., Nair, S., Pavithra, V. et al. Igg4 Related Disease of Skull Base—A Diagnostic Challenge. Indian J Otolaryngol Head Neck Surg 74 (Suppl 2), 1057–1060 (2022). https://doi.org/10.1007/s12070-020-02135-x

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  • DOI: https://doi.org/10.1007/s12070-020-02135-x

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