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Ebstein’s anomaly with total anomalous pulmonary venous connection in an adult

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Indian Journal of Thoracic and Cardiovascular Surgery Aims and scope Submit manuscript

Abstract

Ebstein’s anomaly is a rare congenital cardiac disease which is often associated with various other cardiac anomalies. However, its association with total anomalous pulmonary venous connection is extremely rare with only one case reported so far in the English literature. We report the first successful surgical correction of both Ebstein’s anomaly and total anomalous pulmonary venous connection in an adult patient. Such complex scenarios may pose unique challenges in management which require a judicious approach.

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Authors and Affiliations

Authors

Contributions

JV is the first author who wrote the manuscript and assisted in the surgery. MV is the chief anesthetist who was present in the case and guided in the writing of the manuscript. AS is a senior pediatric cardiologist who referred the case and made relevant corrections in the manuscript. HVJK is the surgical unit chief who performed the surgery and is the corresponding author.

Corresponding author

Correspondence to Honnakere Venkataiya Jayanth Kumar.

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Ethics approval

All procedures performed in this case were in accordance with the ethical standards of the institutional and/or national research committee and with the 1964 Helsinki Declaration and its later amendments or comparable ethical standards.

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Informed written consent was obtained from the patient prior to the study. Written consent was also obtained for the publication of the case report.

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The authors have no conflicts of interest to disclose.

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Vijayan, J., Venkataswamy, M., Subramanian, A. et al. Ebstein’s anomaly with total anomalous pulmonary venous connection in an adult. Indian J Thorac Cardiovasc Surg 40, 369–372 (2024). https://doi.org/10.1007/s12055-023-01664-8

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  • DOI: https://doi.org/10.1007/s12055-023-01664-8

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