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Sporadic right ventricle rhabdomyoma in an adult without tuberous sclerosis

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Indian Journal of Thoracic and Cardiovascular Surgery Aims and scope Submit manuscript

Abstract

Cardiac rhabdomyoma is a rare benign tumor of the pediatric age group which usually regresses by the age of 2 years. Cardiac rhabdomyoma in adults is still a rarer disease. It is usually associated with tuberous sclerosis. Patients with cardiac rhabdomyoma will usually be asymptomatic and detected incidentally, or in suspicion to the signs and symptoms of tuberous sclerosis. Symptomatic patients present with palpitations or failure to thrive due to obstructive symptoms leading to cardiac failure. The authors present a rare case of right ventricular rhabdomyoma in an adult without tuberous sclerosis treated surgically.

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Authors and Affiliations

  1. Department of Cardio Thoracic Vascular Surgery, Institute of Post Graduate Medical Education and Research (IPGME&R), Kolkata, India

    Akash

  2. Department of Cardio Thoracic Vascular Anaesthesiology, Institute of Post Graduate Medical Education and Research (IPGME&R), Kolkata, India

    Pavan Kumar Dammalapati

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  1. Akash
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  2. Pavan Kumar Dammalapati
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Correspondence to Pavan Kumar Dammalapati.

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All procedures performed in this study involving human participants were in accordance with the ethical standards of the institutional research committee and with the 1964 Helsinki Declaration and its later amendments or comparable ethical standards. This article does not contain any studies with animals performed by any of the authors.

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Akash, Dammalapati, P.K. Sporadic right ventricle rhabdomyoma in an adult without tuberous sclerosis. Indian J Thorac Cardiovasc Surg 39, 636–639 (2023). https://doi.org/10.1007/s12055-023-01582-9

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  • DOI: https://doi.org/10.1007/s12055-023-01582-9

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