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A case of tricuspid atresia with pulmonary valve absence coexisting coronary-right ventricular fistula

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Abstract

Tricuspid atresia with pulmonary valve absence is a rare malformation characterized by left ventricular outflow obstruction due to asymmetrical ventricular septal hypertrophy and associated with a poor prognosis. Coexisting coronary-right ventricular fistula is rarely described. We encountered a case of tricuspid atresia with pulmonary valve absence coexisting coronary-right ventricle fistula that successfully underwent Fontan completion. Right ventricle dilatation due to coronary-right ventricle fistula was observed in addition to mass like ventricular septal hypertrophy protruding into the left ventricular outflow tract. Right ventricle reduction and prevention of progressive left ventricular outflow obstruction were achieved by closure of the coronary-right ventricle fistula closure and plication of the right ventricle with the bidirectional Glenn procedure.

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Authors and Affiliations

  1. Department of Cardiovascular Surgery, Kyushu University Hospital, 3-1-1, Maidashi, Higashi-ku, Fukuoka, 812-8582, Japan

    Satoshi Fujita, Hideki Tatewaki & Akira Shiose

  2. Department of Pediatrics, Kyushu University Hospital, Fukuoka, Japan

    Yusaku Nagatomo

Authors
  1. Satoshi Fujita
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  2. Hideki Tatewaki
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  3. Yusaku Nagatomo
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  4. Akira Shiose
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Correspondence to Akira Shiose.

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Fujita, S., Tatewaki, H., Nagatomo, Y. et al. A case of tricuspid atresia with pulmonary valve absence coexisting coronary-right ventricular fistula. Gen Thorac Cardiovasc Surg 69, 1585–1588 (2021). https://doi.org/10.1007/s11748-021-01702-5

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  • DOI: https://doi.org/10.1007/s11748-021-01702-5

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