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A rare case of primary angiosarcoma of the anterior mediastinum

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Abstract

A 32-year-old male patient was initially diagnosed with fibrosing mediastinitis. The patient subsequently developed severe dyspnea and was further diagnosed with constrictive pericarditis due to the extent of fibrosing mediastinitis around the heart. Therefore, the patient underwent surgical resection of the fibrotic tissue in the anterior mediastinum including the pericardium and the pleura. Postoperative histological and immunohistochemical analyses revealed angiosarcoma. Seven years after the diagnosis, he is still alive. Herein, we report a case of atypical primary angiosarcoma of the anterior mediastinum causing constrictive pericarditis and restrictive pulmonary dysfunction.

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Authors and Affiliations

  1. Department of Cardiovascular Surgery, Graduate School of Medicine, Kyoto University, 54 Kawaharacho, Shogoin, Sakyo-ku, Kyoto, Japan

    Kazuhiro Yamazaki, Kenji Minakata, Takeichiro Nakane, Kenji Minatoya & Ryuzo Sakata

  2. Department of Cardiovascular Medicine, Graduate School of Medicine, Kyoto University, Kyoto, Japan

    Hideyuki Kinoshita

  3. Department of Respiratory Medicine, Graduate School of Medicine, Kyoto University, Kyoto, Japan

    Kiminobu Tanizawa

  4. Department of Diagnostic Pathology, Graduate School of Medicine, Kyoto University, Kyoto, Japan

    Shinji Sumiyoshi

  5. Department of Diabetes, Endocrinology and Nutrition, Graduate School of Medicine, Kyoto University, Kyoto, Japan

    Hiroki Sato

Authors
  1. Kazuhiro Yamazaki
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  2. Kenji Minakata
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  3. Takeichiro Nakane
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  4. Hideyuki Kinoshita
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  5. Kiminobu Tanizawa
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  6. Shinji Sumiyoshi
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  7. Hiroki Sato
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  8. Kenji Minatoya
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  9. Ryuzo Sakata
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Correspondence to Kazuhiro Yamazaki.

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Yamazaki, K., Minakata, K., Nakane, T. et al. A rare case of primary angiosarcoma of the anterior mediastinum. Gen Thorac Cardiovasc Surg 69, 766–769 (2021). https://doi.org/10.1007/s11748-020-01551-8

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  • DOI: https://doi.org/10.1007/s11748-020-01551-8

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