Abstract
Juvenile dermatomyositis (JDM) is a rare childhood disease with autoimmune association. Environmental factors are known to trigger JDM in genetically susceptible individuals (Schmieder et al., Dermatol Online 6:3, 2009). Calcinosis is a well-established complication of JDM. Prevalence is higher in children (30–70%; Özkaya et al., Erciyes Med J 30(1):40–43, 2008). Hyperimmunoglobulin E syndrome is a primary immunodeficiency syndrome with multiple recurrent abscess formation and raised serum immunoglobulin E levels. We report a case of JDM with calcinosis cutis universalis with hyperimmunoglobulin E syndrome. With a previous similar case report (Min et al., Korean J Intern Med 14:95–98, 1999), this could well be a new sequence syndrome where abscesses are the trigger for the onset of JDM.
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References
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Saikia, B., Aneja, H., Jain, J. et al. Hyperimmunoglobulin E syndrome with juvenile dermatomyositis and calcinosis. Clin Rheumatol 32 (Suppl 1), 51–53 (2013). https://doi.org/10.1007/s10067-010-1439-x
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DOI: https://doi.org/10.1007/s10067-010-1439-x