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A rare clinical presentation: a pleomorphic xanthoastrocytoma presenting with intracerebral haemorrhage and metastasizing vigorously—case report and review of the literature

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Abstract

Metastasis of an intracranial tumour is not a common situation in our daily neurosurgical practice. Pleomorphic xanthoastrocytoma is also a rare glial tumour with relatively a favourable prognosis among other CNS pathologies. Here, we present an anaplastic pleomorphic xanthoastrocytoma case which shows both haematogenous and lymphatic metastasis which is described first time in the up-to-date literature. Our case is a 17-year-old male operated for a right occipital intra-axial lesion with a diagnosis of anaplastic pleomorphic xanthoastrocytoma which recurs 5 years later and metastasize vigorously through haematogenous and lymphatic routes. A rare-presenting symptom for this pathology is also intracerebral haemorrhage. This is the ninth case report in the literature which presents initially with this entity.

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Acknowledgments

The authors thank Mrs. Özlem Yapıcıer, MD for her contribution for editing figures and details related to pathological headings.

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  1. Division of Pediatric Neurosurgery, Acıbadem University School of Medicine, Altunizade Mah. Yurtcan Sk. NO:1, 34662, Üsküdar/İstanbul, Turkey

    Gülden Demirci Otluoğlu & M. Memet Özek

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  1. Gülden Demirci Otluoğlu
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  2. M. Memet Özek
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Correspondence to Gülden Demirci Otluoğlu.

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Demirci Otluoğlu, G., Özek, M.M. A rare clinical presentation: a pleomorphic xanthoastrocytoma presenting with intracerebral haemorrhage and metastasizing vigorously—case report and review of the literature. Childs Nerv Syst 35, 355–362 (2019). https://doi.org/10.1007/s00381-018-3960-1

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