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A rare case of multicystic disseminated astrocytoma with pilomyxoid characteristics in a 4-year-old child

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Abstract

Pilomyxoid astrocytomas are a more aggressive variant of pilocytic astrocytoma. Over the last 14 years, there has been increasing evidence to suggest that these tumours are distinct pathological entities to pilocytic astrocytomas. Radiological features of these tumours are slowly emerging in the neuroradiological literature. We report a unique radiological appearance of a multicystic, disseminated astrocytoma with pilomyxoid characteristics presenting in a 4-year-old boy and highlight the importance of considering this diagnosis with similar imaging.

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Conflict of interest

The authors report no conflicts of interest. The authors alone are responsible for the content and writing of this paper.

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Authors and Affiliations

  1. Department of Paediatric Neurosurgery, University Hospital of Wales, Cardiff, UK

    S. G. Amarasinghe, H. Ben-ali, R. H. Hatfield & P. A. Leach

  2. Birth Defects Research Centre, UCL Institute of Child Health and Department of Histopathology, Great Ormond Street Hospital for Children NHS Foundation Trust, London, UK

    T. S. Jacques

Authors
  1. S. G. Amarasinghe
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  2. H. Ben-ali
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  3. T. S. Jacques
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  4. R. H. Hatfield
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  5. P. A. Leach
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Corresponding author

Correspondence to S. G. Amarasinghe.

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Amarasinghe, S.G., Ben-ali, H., Jacques, T.S. et al. A rare case of multicystic disseminated astrocytoma with pilomyxoid characteristics in a 4-year-old child. Childs Nerv Syst 31, 625–629 (2015). https://doi.org/10.1007/s00381-014-2566-5

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  • DOI: https://doi.org/10.1007/s00381-014-2566-5

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