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Glomangiomatosis: a case report

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Abstract

Glomangiomatosis is a benign vascular variant of a glomus tumor. The lesion represents only 5% of glomus tumors with unusual or atypical features and even fewer glomus tumors with typical features. The lesions are most commonly located in the distal extremities and are multiple, deep, extensive, and often pain producing. They develop from small arteriovenous anastamoses and are most often identified in young adults. The lesions may recur. We present a case of a 33-year-old male who presented clinically with multiple slowly enlarging masses of the leg over a 5-year period, of which one caused significant pain. One of the lesions was reported to be present at birth. Imaging studies were performed and were suggestive of neurofibromatosis. Biopsies from multiple lesions led to an eventual diagnosis of multiple glomangiomatosis.

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Authors and Affiliations

  1. Department of Pathology and Laboratory Medicine, Rutgers, the State University of New Jersey-New Jersey Medical School, 185 South Orange Avenue, Newark, NJ, 07103, USA

    Valerie A. Fitzhugh

  2. Department of Orthopaedics, Rutgers, the State University of New Jersey-New Jersey Medical School, Newark, NJ, USA

    Kathleen S. Beebe

  3. Department of Radiology, Rutgers, the State University of New Jersey-New Jersey Medical School, Newark, NJ, USA

    Cornelia Wenokor & Marcia Blacksin

Authors
  1. Valerie A. Fitzhugh
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  2. Kathleen S. Beebe
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  3. Cornelia Wenokor
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  4. Marcia Blacksin
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Correspondence to Valerie A. Fitzhugh.

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Fitzhugh, V.A., Beebe, K.S., Wenokor, C. et al. Glomangiomatosis: a case report. Skeletal Radiol 46, 1427–1433 (2017). https://doi.org/10.1007/s00256-017-2697-3

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  • DOI: https://doi.org/10.1007/s00256-017-2697-3

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