Abstract
Primary congenital glaucoma (PCG) is a type of developmental glaucoma, which occurs due to an obstruction in aqueous outflow as a result of abnormal development of the trabecular meshwork and anterior chamber angle. The classic triad for symptoms of PCG includes epiphora, photophobia, and blepharospasm. PCG is usually bilateral (70 to 95%) with uncommon unilateral presentation. PCG can be sporadic, but when inherited, predominantly autosomal recessive mode of inheritance is exhibited. It can be rarely managed medically and surgical options remain the mainstay for intraocular pressure lowering. In this chapter, we demonstrate through various real-life clinical examples, the different clinical presentations and pearls to manage difficult situations arising secondary to PCG.
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Mahalingam, K., Gupta, S. (2023). Primary Congenital Glaucoma. In: Gupta, S., Mahalingam, K., Gupta, V. (eds) Childhood Glaucoma. Springer, Singapore. https://doi.org/10.1007/978-981-19-7466-3_9
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DOI: https://doi.org/10.1007/978-981-19-7466-3_9
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