Takayasu’s Disease with Predominant Pulmonary Arterial Involvement

Abstract

Pulmonary vasculitic syndromes involve the extrapulmonary and intrapulmonary arteries, the parenchymal small vessels (including the capillaries), and bronchial arteries. In the lungs, small-vessel vasculitides (often associated with antineutrophil cytoplasmic antibody positivity) are more common. Involvement of the pulmonary vasculature by large-vessel or medium-sized vessel vasculitis is distinctly rare. A young male patient presented with clinical features of thromboembolism. Autopsy revealed Takayasu’s arteritis which had a dominant involvement of the pulmonary artery with a clinically insignificant aortic disease.