Abstract
Arrhythmogenic Cardiomyopathy refers to a genetically inherited nonischemic disorder, characterized by univentricular and/or biventricular myocardial fibrous or fibro-fatty replacement. In most cases, the disorder is inherited as an autosomal disease caused by mutations in the several desmosomal proteins. Importantly, the cardiomyopathy carries an inherent capability to induce ventricular arrhythmias even before the development of the morphological changes. A young man, who had persistent hypotension, died suddenly and the autopsy revealed the presence of biventricular (right ventricular dominant) arrhythmogenic cardiomyopathy.
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Further Reading
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Vaideeswar, P. (2022). Arrhythmogenic Cardiomyopathy. In: Vaideeswar, P. (eds) Tropical Cardiovascular Pathology. Springer, Singapore. https://doi.org/10.1007/978-981-19-3720-0_44
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DOI: https://doi.org/10.1007/978-981-19-3720-0_44
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