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Long-Term Complications: Hepatopulmonary Syndrome

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Introduction to Biliary Atresia

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Abstract

Hepatopulmonary syndrome (HPS) is a disease of gas exchange caused by intrapulmonary shunting secondary to liver disease-associated intrapulmonary vascular dilation [1]. HPS is characterized by the triad of arterial deoxygenation, intrapulmonary vascular dilatation, and liver disease, all of which occur in the absence of a primary cardiopulmonary anomaly. Liver diseases that are commonly involved include cirrhosis, portal hypertension, and portosystemic shunt [2]. HPS is not correlated with cirrhosis severity and can be caused even by asymptomatic cirrhosis [3]. HPS may also develop in noncirrhotic portal hypertension [4].

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Authors and Affiliations

  1. Osaka University, Osaka, Japan

    Takehisa Ueno

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  1. Takehisa Ueno
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Correspondence to Takehisa Ueno .

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  1. Department of Pediatric Surgery, Tohoku University Graduate School of Medicine, Sendai, Japan

    Masaki Nio

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Ueno, T. (2021). Long-Term Complications: Hepatopulmonary Syndrome. In: Nio, M. (eds) Introduction to Biliary Atresia. Springer, Singapore. https://doi.org/10.1007/978-981-16-2160-4_35

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  • DOI: https://doi.org/10.1007/978-981-16-2160-4_35

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