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Imaging of Single Ventricle

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CT and MRI in Congenital Heart Diseases

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Abstract

Single ventricle is a unique entity with a complex anatomy and physiology where there is complete or partial absence of an interventricular septum. It is associated with high morbidity, mortality and resource usage. The palliation of this condition generally involves a univentricular repair which involves a creation of a complete cavopulmonary connection by incorporating the caval flow into the pulmonary circulation. The key to a successful procedure revolves around a preoperative comprehensive multimodality cardiac imaging. Multiple imaging techniques are used in a graded and complementary fashion in order to select the right patient for the Fontan procedure and to ensure good long-term outcomes. Echocardiography, cardiac MRI and cardiac CTA are the tools that are frequently used in the evaluation of this disease entity. Proper application of existing and novel techniques will hopefully make this complex evaluation simpler and ultimately lead to better outcomes.

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Author information

Authors and Affiliations

  1. CARE Hospitals, Hyderabad, India

    Johann Christopher & Sudeep Verma

  2. Department of Radiology, Amrita School of Medicine, Amrita Institute of Medical Sciences and Research Centre, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

    Ramiah Rajeshkannan

Authors
  1. Johann Christopher
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  2. Sudeep Verma
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  3. Ramiah Rajeshkannan
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Editor information

Editors and Affiliations

  1. Department of Radiology, Amrita School of Medicine, Amrita Institute of Medical Sciences and Research Centre, Amrita Vishwa Vidyapeetham, Kochi, Kerala, India

    Ramiah Rajeshkannan

  2. Department of Cardiothoracic imaging, Narayana Hrudayalaya, Bangalore, Karnataka, India

    Vimal Raj

  3. Department of Radiology, Sri Sathya Sai Institute of Higher Medical Sciences, Bengaluru, Karnataka, India

    Sanjaya Viswamitra

1 Electronic Supplementary Material

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3D heart

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3D heart

Ax cine post Fontan

Ax cine Pre Fontan

Cor cine post Fonatn

Fontan PC

MRA post Fontan

MRA preFontan

Sag cine post Fonatn

2C herniation

3D MRA moving

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CMR 4 chamber view in a case of tricuspid atresia (MP4 1964 kb)

4Ch cine

Aortic outflow

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MRA

Pulmonary outflow cine

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Video 17.1

CMR in 13 years old boy. Single ventricle of LV morphology, hypo plastic RV, large inlet VSD and normally related great arteries. Status post BDGS and atrial septectomy for Fontan completion (PDF 827 kb)

Video 17.4

CMR in 11 years old girl. S L L, DILV, L posed aorta from hypo plastic RV with restrictive bulbo-ventricular foramen. Status post Fontan surgery (PDF 1179 kb)

Video 17.8

CMR in 11 years old girl. Heterotaxy, tricuspid atresia, DORV, hypo plastic RV. Status post bilateral BDGS for Fontan completion (PDF 824 kb)

Video 17.17

CMR in 15 years old boy. Single ventricle, common AV valve, severe pulmonary stenosis, cardiac herniation and cor triatriatum. Status post BDGS (PDF 3776 kb)

Video 17.24

CMR in 14 years old girl. DILV with Supra mitral ring and intact atrial septum, Restrictive bulbo-ventricular foramen with sub aortic obstruction. Status post BDGS (PDF 22 kb)

Video 17.32

CMR in 13 years old girl. DILV, normally related great arteries, moderate pulmonary stenosis, PAH (PDF 1484 kb)

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Christopher, J., Verma, S., Rajeshkannan, R. (2021). Imaging of Single Ventricle. In: Rajeshkannan, R., Raj, V., Viswamitra, S. (eds) CT and MRI in Congenital Heart Diseases. Springer, Singapore. https://doi.org/10.1007/978-981-15-6755-1_17

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  • DOI: https://doi.org/10.1007/978-981-15-6755-1_17

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