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Ebstein’s Anomaly in the Adult: Timing for Surgical Intervention in Adult Population

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Adult Congenital Heart Disease

Abstract

Ebstein’s anomaly (EA) is a rare congenital cardiac malformation, and this anomaly is a disorder of a tricuspid valve (TV) development in which the valve leaflets fail to delaminate properly from the ventricular wall. Clinical symptoms are age dependent and include cyanosis (size of interatrial communication), right-sided heart failure, arrhythmias, and general fatigue on exercise. Optimal timing of surgical intervention is often difficult and must be individualized. Patients have good long-term survival and functional outcomes after undergoing surgery for Ebstein anomaly in adult population. Operation includes tricuspid valve repair or replacement, closure of any interatrial communications, and appropriate antiarrhythmia procedures.

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Acknowledgment

I am grateful to Dr. Munetaka Masuda for providing Fig. 14.6.

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Authors and Affiliations

  1. Department of Cardiovascular Surgery, Okayama University Graduate School of Medicine, Dentistry and Pharmaceutical Sciences, Okayama, Japan

    Shingo Kasahara M.D., Ph.D.

Authors
  1. Shingo Kasahara M.D., Ph.D.
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Correspondence to Shingo Kasahara M.D., Ph.D. .

Editor information

Editors and Affiliations

  1. Department of Surgery, Yokohama City Univ. Grad. School of Med., Yokohama, Kanagawa, Japan

    Munetaka Masuda

  2. Cardiovascular Center, St Luke’s International Hospital, Tokyo, Japan

    Koichiro Niwa

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Kasahara, S. (2017). Ebstein’s Anomaly in the Adult: Timing for Surgical Intervention in Adult Population. In: Masuda, M., Niwa, K. (eds) Adult Congenital Heart Disease. Springer, Singapore. https://doi.org/10.1007/978-981-10-4542-4_14

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  • DOI: https://doi.org/10.1007/978-981-10-4542-4_14

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  • Publisher Name: Springer, Singapore

  • Print ISBN: 978-981-10-4541-7

  • Online ISBN: 978-981-10-4542-4

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