Abstract
Among connective tissue diseases (CTDs), lupus is most common in childhood. Localized scleroderma is much more common than systemic sclerosis, and juvenile dermatomyositis is by far the most frequent form of idiopathic inflammatory myositis seen in the pediatric age group. These diseases should be distinguished from infections, malignancies, and mimics. The case vignettes described in this chapter discuss the presentations of children with suspected CTDs with take home messages at the end of each case.
This is a preview of subscription content, log in via an institution to check access.
Access this chapter
Tax calculation will be finalised at checkout
Purchases are for personal use only
Similar content being viewed by others
References
Biner B, Acunaş B, Karasalihoğlu S, Vatansever U. Systemic lupus erythematosus presenting with generalized lymphadenopathy: a case report. Turk J Pediatr. 2001;43:94–6.
Ziaee V, Yeganeh MH, Moradinejad MH. Peripheral gangrene: a rare presentation of systemic lupus erythematosus in a child. Am J Case Rep. 2013;14:337–40.
Zulian F, Corona F, Gerloni V, Falcini F, Buoncompagni A, Scarazatti M, Martini G, Zacchello F. Safety and efficacy of iloprost for the treatment of ischaemic digits in paediatric connective tissue diseases. Rheumatology (Oxford). 2004;43:229–33.
Rani JD, Patil SG, Murthy ST, Koshy AV, Nagpal D, Gupta S. Juvenile scleredema of Buschke. J Contemp Dent Pract. 2012;13:111–4.
Shrestha B, Neopane AK, Panth R. Scleredema–an uncommon cause of swelling in a child–a case report and review of the literature. BMC Res Notes. 2014;7:571.
Dogra S, Handa S, Kanwar AJ. Dexamethasone pulse therapy for scleredema. Pediatr Dermatol. 2004;21:280–1.
RodrÃguez Soriano J. Renal tubular acidosis: the clinical entity. J Am Soc Nephrol. 2002;13:2160–70.
Pessler F, Emery H, Dai L, Wu YM, Monash B, Cron RQ, Pradhan M. The spectrum of renal tubular acidosis in paediatric Sjögren syndrome. Rheumatology (Oxford). 2006;45:85–91.
Saini I, Kalaivani M, Kabra SK. Calcinosis in juvenile dermatomyositis: frequency, risk factors and outcome. Rheumatol Int. 2016. [Epub ahead of print].
Marco Puche A, CalvoPenades I, Lopez Montesinos B. Effectiveness of the treatment with intravenous pamidronate in calcinosis in juvenile dermatomyositis. Clin Exp Rheumatol. 2010;28:135–40.
Cañas CA, Bonilla-AbadÃa F, MejÃa M, Tobón GJ. Recovery of severe muscular and fascial calcinosis after treatment with bisphosphonates in a child with juvenile dermatomyositis. J Clin Rheumatol. 2015;21:267–9.
Author information
Authors and Affiliations
Corresponding author
Editor information
Editors and Affiliations
Rights and permissions
Copyright information
© 2017 Springer Science+Business Media Singapore
About this chapter
Cite this chapter
Gupta, R., Aggarwal, A. (2017). Clinical Case Vignettes: Connective Tissue Diseases in Children. In: Sawhney, S., Aggarwal, A. (eds) Pediatric Rheumatology. Springer, Singapore. https://doi.org/10.1007/978-981-10-1750-6_32
Download citation
DOI: https://doi.org/10.1007/978-981-10-1750-6_32
Published:
Publisher Name: Springer, Singapore
Print ISBN: 978-981-10-1749-0
Online ISBN: 978-981-10-1750-6
eBook Packages: MedicineMedicine (R0)