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Vestibular Neuropathy

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Cochlear Implantation in Children with Inner Ear Malformation and Cochlear Nerve Deficiency

Part of the book series: Modern Otology and Neurotology ((MODOTOL))

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Abstract

Auditory neuropathy is a disorder which is defined as hearing loss combined with severe abnormalities of auditory brainstem responses (ABRs) in the presence of preserved cochlear outer hair cell function indicated by normal evoked otoacoustic emissions (OAEs) and/or cochlear microphonics. On the other hand, neuropathies of the vestibular nerves have not been commonly recognized. One reason for this situation may be due to ambiguity in the definition of vestibular neuropathy, since until recently there were no vestibular tests such as ABR or DPOAE which can discriminate between labyrinthine and retrolabyrinthine lesions. Another reason is that some patients with bilateral vestibular dysfunction do not express symptoms of a vestibular disorder. Currently, vestibular neuropathy is usually diagnosed from circumstantial evidence. This chapter describes (1) vestibular dysfunction in patients with auditory neuropathy, (2) vestibular involvement in other neuropathies, and (3) retrolabyrinthine involvement in idiopathic bilateral vestibulopathy, in the literature as well as in our experience. This review concludes that many patients with auditory neuropathy or other neuropathies also have bilateral vestibular dysfunction.

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Authors and Affiliations

  1. Department of Otorhinolaryngology, Head and Neck Surgery, Graduate School of Medicine, The University of Tokyo, 7-3-1 Hongo, Bunkyo-ku, Tokyo, 113-8655, Japan

    Shinichi Iwasaki M.D.

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  1. Shinichi Iwasaki M.D.
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Correspondence to Shinichi Iwasaki M.D. .

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Editors and Affiliations

  1. National Institute of Sensory Organs, National Tokyo Medical Center, Tokyo, Japan

    Kimitaka Kaga

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Iwasaki, S. (2017). Vestibular Neuropathy. In: Kaga, K. (eds) Cochlear Implantation in Children with Inner Ear Malformation and Cochlear Nerve Deficiency. Modern Otology and Neurotology. Springer, Singapore. https://doi.org/10.1007/978-981-10-1400-0_9

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  • DOI: https://doi.org/10.1007/978-981-10-1400-0_9

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  • Publisher Name: Springer, Singapore

  • Print ISBN: 978-981-10-1399-7

  • Online ISBN: 978-981-10-1400-0

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