Abstract
In pulmonary atresia intact ventricular septum, or hypoplastic right heart syndrome the blood that enters the right ventricle has no egress, so regurgitate back into right atrium via tricuspid valve, and reach the left atrium through foramen ovale. These patients may have coronary sinusoidal channels. Echocardiography is useful in evaluating the right ventricular and tricuspid annulus size and may show sinusoidal channels, but angiography is necessary to evaluate the RV-dependent coronary circulation, and make the best decision for patient.
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Ghaffari, S., Moradian, M. (2021). Pulmonary Valve Atresia, Intact Ventricular Septum (PA IVS) or Hypoplastic Right Heart Syndrome (HRHS). In: Moradian, M., Alizadehasl, A. (eds) Atlas of Echocardiography in Pediatrics and Congenital Heart Diseases. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-62341-1_26
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DOI: https://doi.org/10.1007/978-3-662-62341-1_26
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