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Systemischer Lupus erythematodes und seltene rheumatische Krankheiten

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Pädiatrie

Part of the book series: Springer Reference Medizin ((SRM))

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Zusammenfassung

Der systemische Lupus erythemathodes (SLE) ist eine B-Zell-vermittelte, chronisch-entzündliche Autoimmunkrankheit, die gekennzeichnet ist durch Produktion von Autoantikörpern gegen Zellkernbestandteile und Ablagerung von Immunkomplexen, die eine Vaskulitis verursachen. Zahlreiche Organe können betroffen sein, z. B. Haut, Niere, Lunge und ZNS. Die frühe Manifestation eines SLE ist häufig mit einem schweren Verlauf assoziiert. Zu den hier besprochenen seltenen rheumatischen Erkrankungen gehören mixed connective tissue disease, Sjögren-Syndrom und eosinophile Fasziitis.

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Author information

Authors and Affiliations

  1. Klinik für Kinder- und Jugendmedizin, Universitätsklinik Aachen, Aachen, Deutschland

    Norbert Wagner

  2. Kinderrheumatologische Ambulanz, Charite – Universitätsmedizin Berlin, Berlin, Deutschland

    Günther Dannecker

Authors
  1. Norbert Wagner
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  2. Günther Dannecker
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Corresponding author

Correspondence to Norbert Wagner .

Editor information

Editors and Affiliations

  1. Zentrum für Kinder und Jugendmedizin, Universitätsklinikum Heidelberg, Heidelberg, Germany

    Georg F. Hoffmann

  2. Bonn, Germany

    Michael J. Lentze

  3. Sinzheim, Germany

    Jürgen Spranger

  4. Zentrum für Kinder- und Jugendmedizin, Universitätsmedizin Mainz, Mainz, Germany

    Fred Zepp

  5. Klinik und Poliklinik für Kinder- und Jugendmedizin, Universitätsklinikum Carl Gustav Carus an der Technischen Universität Dresden, Dresden, Germany

    Reinhard Berner

Section Editor information

  1. Klinik und Poliklinik für Kinder- und Jugendmedizin, Universitätsklinikum Carl Gustav Carus Dresden an der Technischen Universität Dresden, Dresden, Deutschland

    Reinhard Berner

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Wagner, N., Dannecker, G. (2020). Systemischer Lupus erythematodes und seltene rheumatische Krankheiten. In: Hoffmann, G.F., Lentze, M.J., Spranger, J., Zepp, F., Berner, R. (eds) Pädiatrie. Springer Reference Medizin. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-60300-0_106

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  • DOI: https://doi.org/10.1007/978-3-662-60300-0_106

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  • Publisher Name: Springer, Berlin, Heidelberg

  • Print ISBN: 978-3-662-60299-7

  • Online ISBN: 978-3-662-60300-0

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