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Skelettveränderungen bei Erkrankungen des retikulohistiozytären Systems

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Skeletterkrankungen

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Zusammenfassung

Erkrankungen des retikulohistiozytären Systems können – seinen verschiedenartigen Aufgaben und zellulären Zusammensetzung entsprechend – ein breites Spektrum von Krankheiten im muskuloskelettalen Apparat auslösen, zu denen so seltene erbliche Krankheitsbilder wie Lipid- und Glykogenspeicherkrankheiten, aber auch geläufige Erkrankungen wie die Langerhans-Zell-Histiozytose und die Mastozytose zählen. Die seltene Lipoidgranulomatose zählt man heute zu den Non-Langerhans-Zell-Histiozytosen. Die radiologischen Veränderungen am Knochen sind vielschichtig und in den meisten Fällen sehr spezifisch.

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  1. Klinikum Bremen-Mitte Beratungsstelle und Referenzzentrum, Bremen

    J. Freyschmidt

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Freyschmidt, J. (2016). Skelettveränderungen bei Erkrankungen des retikulohistiozytären Systems. In: Skeletterkrankungen. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-662-48137-0_8

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