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ADAMTS13 endopeptidase 3.4.24.87

  • Chapter
Class 3.4–6 Hydrolases, Lyases, Isomerases, Ligases

Part of the book series: Springer Handbook of Enzymes ((HDBKENZYMES,volume 10))

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Nomenclature

EC number

 3.4.24.87

Recommended name

 ADAMTS13 endopeptidase

Synonyms

 ADAMTS 13 <3> [59,90]

 ADAMTS VWF cleaving metalloprotease <3> [3]

 ADAMTS-13 <2,3,4> (<3> i.e. a disintegrin and metalloprotease with a thrombospondin type 1 motifs 13 [75]) [1,4,5,25,26,30,40,42,43,44,45,47,69,75,79,91]

 ADAMTS13 <1,2,3,4,5,6,7,8,9,10> (<3> i.e. a disintegrin and metalloprotease with thrombospondin repeats [6,12]; <3> ADAMTS13 belongs to the ADAMTS or a disintegrin-like and metalloproteinase with thrombospondin type-1 motif family [97]; <3> ADAMTS13 is a member of the a disintegrin and metalloprotease with thrombospondin type 1 repeats, i.e. ADAMTS, family [63]; <3> i.e a disintegrin and metalloprotease with thrombospondin 13 [92]; <2> i.e. a disintegrin and metalloprotease with thrombospondin domain 13 [76]; <3> i.e. a disintegrin and metalloprotease with thrombospondin motif [78]; <3> i.e. a disintegrin and metalloprotease with thrombospondin motifs-13 [68]; <2,3> i.e. a disintegrin-like and metalloprotease with trombospondin type-1 repeats 13 [67,101,102]; <3> i.e. disintegrin-like domain and Metalloprotease with ThromboSpondin type I motif 13 [99]) [2,3,6,10,11,12,13,16,21,22,28,31,32,33,34,35,36,37,38,39,41,46,48,49,50,52,53,-54,55,56,57,58,60,61,62,63,64,65,66,67,68,70,71,72,73,74,76,77,78,80,81,82,83,8-5,86,87,88,89,92,93,94,95,96,97,98,99,100,101,102,103,104,105,106]

 ADAMTS13 metalloprotease <3> [60,66]

 M12.241 <3,9> (<3,9> Merops-ID [1,2,3,4,5,6,7,8,9,10,11,12,13]) [1,2,3,4,5,6,7,8,9,10,11,12,13]

 Upshaw factor <3> [1]

 VWF cleaving metalloprotease <3> [3]

 VWF cleaving protease <3> [1,33,39,49,57]

 VWF-CP <3> [4,13,39]

 VWF-cleaving metalloprotease <3> [83]

 VWFCP <9> [10]

 a disintegrin and metalloprotease with thrombospondin motifs 13 <3> [38]

 a disintegrin and metalloprotease with thrombospondin-13 <4> [25]

 a disintegrin and metalloproteinase with a thrombonspondin type 1 motif member 13 <3> [44]

 a disintegrin-like and metalloprotease with thrombospondin type I repeats - 13 <10> [53]

 a disintegrin-like and metalloprotease with thrombospondin type-1 motifs 13 <3> [94]

 a disintegrin-like and metalloproteinase domain with thrombospondin type I motifs 13 <3> [83]

 a disintegrin-like domain and metalloprotease with thrombospondin type I motif <3> [48]

 metalloprotease ADAMTS-13 <3> [59]

 plasma metalloprotease ADAMTS13 <1,2,3,4,5,6,7,8> [89]

 plasma von Willebrand factor cleaving activity <3> [37]

 vWF protease <3> [9]

 vWF-cleaving protease <3> [8,13,42,43,56,94,99,103]

 vWF-degrading protease <3> [7]

 van Willebrand factor processing activity <3> [1]

 von Willebrand cleavage protease <3> [95]

 von Willebrand factor cleaving protease <3> [1,33,49,57,94]

 von Willebrand factor-cleaving metalloprotease <3> [83]

 von Willebrand factor-cleaving protease <2,3,9> [2,4,5,9,10,13,14,31,39,42,43,48,67,94,103]

 von Willebrand factor-cleaving proteinase <9> [55]

 von-Willebrand factor cleaving protease <3> [11,12]

 von-Willebrand factor degrading protease <3> [7]

 von-Willebrand-factor-cleaving protease <3> [28]

 xWF-CP <3> [14]

 Additional information <3,9> (<3> a disintegrin and metalloprotease with thrombospondin type 1 motif, member 13 [35]; <3> a disintegrin and metalloprotease with trombonspondin motif 13 [37]; <3> ADAMTS13 belongs to the family of a disintegrin-like and metalloprotease domains with repeated thrombospondin domains [104]; <3> ADAMTS13 is a member of a disintegrin and metalloprotease with thrombospondin type 1 repeats, ADAMTS, family [73]; <3> ADAMTS13 is a member of the ADAMTS, a disintegrin and metalloproteinase with thrombospondin motifs, family of proteins [95]; <9> ADAMTS13 is a reprolysin-type metalloproteinase belonging to the ADAMTS, i.e. a disintegrin and metalloproteinase with thrombospondin type 1 motif, family [55]) [35,37,55,73,95,104]

CAS registry number

 334869-10-2

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Schomburg, D., Schomburg, I. (2013). ADAMTS13 endopeptidase 3.4.24.87. In: Schomburg, D., Schomburg, I. (eds) Class 3.4–6 Hydrolases, Lyases, Isomerases, Ligases. Springer Handbook of Enzymes, vol 10. Springer, Berlin, Heidelberg. https://doi.org/10.1007/978-3-642-36260-6_8

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