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Cardiopulmonary Exercise and Six-Minute Walk Testing

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Pulmonary Hypertension in Adult Congenital Heart Disease

Part of the book series: Congenital Heart Disease in Adolescents and Adults ((CHDAA))

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Abstract

Cardiopulmonary exercise testing (CPEX) and the six-minute walk testing (6MWT) enable the detailed functional evaluation of patients with pulmonary hypertension secondary to congenital heart disease. These tests can be used for symptom evaluation, assessment of intervention and a guideline to prognosis. A good understanding of the physiology of cardiopulmonary exercise testing is a prerequisite for the optimal care of the adult with pulmonary hypertension secondary to congenital heart disease.

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Abbreviations

ACCP:

American College of Chest Physicians

ACHD:

Adult Congenital Heart Disease

AT:

Anaerobic threshold

ATS:

American Thoracic Society

BP:

Blood pressure

CO2 :

Carbon dioxide

CPEX:

Cardiopulmonary exercise testing

DO2 :

Peripheral oxygen delivery

HCO3 :

Bicarbonate

HF-PEF:

Heart failure with preserved ejection fraction

MVV:

Maximum voluntary ventilation

NYHA:

New York Heart Association

OUER:

Oxygen Uptake Extraction Ratio

OUES:

Oxygen Uptake Efficiency Slope

PAP:

Pulmonary arterial pressure

PetCO2 :

end tidal CO2

PH:

Pulmonary hypertension

PH–ACHD:

Pulmonary hypertension related to Adult Congenital Heart Disease

RER:

Respiratory exchange ratio

VCO2 :

CO2 production

VD:

Dead space

VE:

Ventilation

VO2 :

Oxygen consumption

VT:

Tidal volume

WR:

Work rate

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Author information

Authors and Affiliations

  1. Bristol Heart Institute and Bristol Royal Hospital for Children, Marlborough St, Bristol, BS2 8HW, UK

    Graham Stuart M.B.Ch.B., M.Sc., F.R.C.P. & Reza Ashrafi M.B.B.S., B.Sc., M.R.C.P.

Authors
  1. Graham Stuart M.B.Ch.B., M.Sc., F.R.C.P.
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  2. Reza Ashrafi M.B.B.S., B.Sc., M.R.C.P.
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Corresponding author

Correspondence to Graham Stuart M.B.Ch.B., M.Sc., F.R.C.P. .

Editor information

Editors and Affiliations

  1. Adult Congenital Heart Centre and Centre for Pulmonary Hypertension, Royal Brompton Hospital and Imperial College, London, United Kingdom

    Konstantinos Dimopoulos

  2. University Hospital, Münster, Germany

    Gerhard-Paul Diller

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Stuart, G., Ashrafi, R. (2017). Cardiopulmonary Exercise and Six-Minute Walk Testing. In: Dimopoulos, K., Diller, GP. (eds) Pulmonary Hypertension in Adult Congenital Heart Disease. Congenital Heart Disease in Adolescents and Adults. Springer, Cham. https://doi.org/10.1007/978-3-319-46028-4_13

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  • DOI: https://doi.org/10.1007/978-3-319-46028-4_13

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-46026-0

  • Online ISBN: 978-3-319-46028-4

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