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The “Connective Tissue Diseases”

  • Living reference work entry
  • First Online:
Atlas of Dermatology, Dermatopathology and Venereology

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Abstract

Autoimmune connective tissue diseases are a group of disorders with heterogeneous clinical manifestations; however, they share one common feature, namely, inflammation of connective tissue. In some of these diseases, such as morphea or lichen sclerosus, the disease is limited to the skin, while in others, such as in dermatomyositis, systemic sclerosis, or systemic lupus erythematosus, skin lesions are only one of the possible manifestations of the disease, and the severity of the disease depends on which organs are involved. In this chapter we have focused on the most meaningful skin symptoms, which should help the clinicians and histopathologists making the proper diagnosis; however, we have also included less commonly observed clinical variants to illustrate a wide clinical spectrum of connective tissue diseases.

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Authors and Affiliations

  1. Department of Dermatology, University of Rzeszow, Rzeszów, Poland

    Adam Reich, Dominik Samotij & Justyna Szczęch

  2. Department of Health Sciences, Section of Dermatology, University of Florence, Florence, Italy

    Emiliano Antiga

  3. Department of Dermatology, Poznan University of Medical Sciences, Poznań, Poland

    Monika Bowszyc-Dmochowska & Aleksandra Dańczak-Pazdrowska

  4. Department of Dermatology and Venereology, Poznan University of Medical Sciences, Poznań, Poland

    Adriana Polańska

  5. Department and Clinic of Rheumatology and Internal Medicine, Wroclaw Medical University, Wrocław, Poland

    Renata Sokolik & Magdalena Szmyrka

  6. Department of Pathomorphology, Wroclaw Medical University, Wrocław, Poland

    Zdzisław Woźniak

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  1. Adam Reich
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Correspondence to Adam Reich , Emiliano Antiga , Monika Bowszyc-Dmochowska , Aleksandra Dańczak-Pazdrowska , Adriana Polańska , Dominik Samotij , Renata Sokolik , Justyna Szczęch , Magdalena Szmyrka or Zdzisław Woźniak .

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  1. Department of Pathology, Univ of Rochester School of Med, Rochester, NY, USA

    Bruce Smoller

  2. Khorramshahr, Iran

    Nooshin Bagherani

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Reich, A. et al. (2020). The “Connective Tissue Diseases”. In: Smoller, B., Bagherani, N. (eds) Atlas of Dermatology, Dermatopathology and Venereology . Springer, Cham. https://doi.org/10.1007/978-3-319-45134-3_43-1

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  • DOI: https://doi.org/10.1007/978-3-319-45134-3_43-1

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