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Fontan

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Pregnancy and Congenital Heart Disease

Part of the book series: Congenital Heart Disease in Adolescents and Adults ((CHDAA))

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Abstract

Incidence: The Fontan operation is a palliative procedure for patients with tricuspid atresia, double-inlet ventricle, double-outlet ventricle, pulmonary atresia with intact septum and hypoplastic left heart syndrome, all rare congenital lesions. About 5 % of all patients with congenital heart disease need a Fontan operation.

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Abbreviations

ACC:

American College of Cardiology

AHA:

American Heart Association

BP:

Blood pressure

CHD:

Congenital heart disease

CO:

Cardiac output

CPET:

Cardiopulmonary exercise test

CT:

Computed tomography

ECG:

Electrocardiogram

EF:

Ejection fraction

FC:

Fontan circulation

LMWH:

Low molecular weight heparin

MR:

Magnetic resonance

NYHA:

New York Heart Association

SVT:

Supraventricular tachycardia

TCPC:

Total cavopulmonary conversion

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Author information

Authors and Affiliations

  1. Adult Congenital Heart Centre and Centre for Pulmonary Hypertension, Royal Brompton Hospital, London, UK

    Margherita Ministeri MD & Michael A. Gatzoulis MD, PhD, FACC, FESC

  2. National Heart & Lung Institute, Imperial College, London, UK

    Margherita Ministeri MD & Michael A. Gatzoulis MD, PhD, FACC, FESC

  3. Division of Cardiology, Ferrarotto Hospital, University of Catania, Catania, Italy

    Margherita Ministeri MD

Authors
  1. Margherita Ministeri MD
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  2. Michael A. Gatzoulis MD, PhD, FACC, FESC
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Corresponding author

Correspondence to Margherita Ministeri MD .

Editor information

Editors and Affiliations

  1. Erasmus MC University Medical Center, Rotterdam, Gelderland, The Netherlands

    Jolien W. Roos-Hesselink

  2. Chelsea and Westminster Hospital, London, United Kingdom

    Mark R. Johnson

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Ministeri, M., Gatzoulis, M.A. (2017). Fontan. In: Roos-Hesselink, J., Johnson, M. (eds) Pregnancy and Congenital Heart Disease. Congenital Heart Disease in Adolescents and Adults. Springer, Cham. https://doi.org/10.1007/978-3-319-38913-4_15

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  • DOI: https://doi.org/10.1007/978-3-319-38913-4_15

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-38911-0

  • Online ISBN: 978-3-319-38913-4

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