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Changing Epidemiology of Congenital Heart Disease

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Congenital Heart Disease and Adolescence

Part of the book series: Congenital Heart Disease in Adolescents and Adults ((CHDAA))

Abstract

Epidemiology is the study of the frequency and distribution of disease. The most commonly reported birth prevalence rates of congenital heart disease (CHD) vary from 5 to 15 per 1000 live births with a 10–15 % proportion of severe or complex lesions. Adults now account for two thirds of all CHD patients with a rapid expansion of the adolescent age group. Patients with CHD have improved mortality and survival, but life expectancy, for which there is little data, is likely the most important measure of disease burden for adolescents. Boys and men have a higher mortality and morbidity from infancy to adulthood compounded by underutilization of elective health services. It has now been shown that specialized adults with congenital heart disease (ACHD) care improves mortality, yet the majority of patients are not being followed in specialized centers. Age-specific processes of care referral need to be elaborated to improve follow-up and minimize lapses in care.

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Author information

Authors and Affiliations

  1. McGill Adult Unit for Congenital Heart Disease Excellence (MAUDE Unit), McGill University Health Center, 1001 Decarie Boulevard, Montreal, QC, Canada

    Efrat Mazor Dray & Ariane J. Marelli MD, MPH, FRCPC, FACC, FAHA

  2. Department of Cardiology, Soroka University Medical Center, Ben Gurion University of the Negeve, Beer-Sheva, Israel

    Efrat Mazor Dray

Authors
  1. Efrat Mazor Dray
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  2. Ariane J. Marelli MD, MPH, FRCPC, FACC, FAHA
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Corresponding author

Correspondence to Ariane J. Marelli MD, MPH, FRCPC, FACC, FAHA .

Editor information

Editors and Affiliations

  1. Center for Congenital Heart Disease, University Hospital Inselspital, Bern, Switzerland

    Markus Schwerzmann

  2. Center for Congenital Heart Disease, University Hospital Inselspital, Bern, Switzerland

    Corina Thomet

  3. Department of Public Health and Primary Care, KU Leuven – University of Leuven, Leuven, Belgium and Institute of Health and Care Sciences, University of Gothenburg, Gothenburg, Sweden

    Philip Moons

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Dray, E.M., Marelli, A.J. (2016). Changing Epidemiology of Congenital Heart Disease. In: Schwerzmann, M., Thomet, C., Moons, P. (eds) Congenital Heart Disease and Adolescence. Congenital Heart Disease in Adolescents and Adults. Springer, Cham. https://doi.org/10.1007/978-3-319-31139-5_1

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  • DOI: https://doi.org/10.1007/978-3-319-31139-5_1

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-31137-1

  • Online ISBN: 978-3-319-31139-5

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