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Prune Belly Syndrome

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Congenital Anomalies of the Kidney and Urinary Tract

Abstract

Prune belly syndrome was first described in 1895. The syndrome consists of the triad of a thin flaccid, wrinkled, abdominal wall; undescended, intraabdominal testicles; and bladder enlargement with hydroureters. Developmental etiology is unknown with consideration given to both obstructive and mesodermal defects. Evaluation requires assessment of pulmonary and renal function along with other associated system disorders. Treatment should be focused on preservation of renal function through management of stagnant urine and prevention of UTIs. Operative intervention when required is discussed and includes the upper and lower urinary tract, the testicles, and the appearance of the abdominal wall.

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Abbreviations

PBS:

Prune belly syndrome

UTI:

Urinary tract infection

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Author information

Authors and Affiliations

  1. Department of Urology, The University of Alabama at Birmingham, 1600 7th Ave South, Birmingham, AL, USA

    David B. Joseph M.D., F.A.C.S., F.A.A.P.

Authors
  1. David B. Joseph M.D., F.A.C.S., F.A.A.P.
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Correspondence to David B. Joseph M.D., F.A.C.S., F.A.A.P. .

Editor information

Editors and Affiliations

  1. Department of Pediatrics, Georgetown University Medical Center, Washington, District of Columbia, USA

    Amin J. Barakat

  2. Division of Pediatric Urology, Children’, George Washington University School of M, Washington, District of Columbia, USA

    H. Gil Rushton

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© 2016 Springer International Publishing Switzerland

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Joseph, D.B. (2016). Prune Belly Syndrome. In: Barakat, A., Rushton, H. (eds) Congenital Anomalies of the Kidney and Urinary Tract. Springer, Cham. https://doi.org/10.1007/978-3-319-29219-9_10

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  • DOI: https://doi.org/10.1007/978-3-319-29219-9_10

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-319-29217-5

  • Online ISBN: 978-3-319-29219-9

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