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Epidemiology of Pulmonary Hypertension: From Quaternary Referral Centre to the Community

  • Chapter
Pulmonary Hypertension

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Abstract

Pulmonary arterial hypertension (PAH) in its classic form is a rare progressive disease affecting predominantly young women. The first clinical classification system for pulmonary hypertension (PH) was put forth in Evian, France in 1998 in order to categorize alternate forms of pulmonary vascular disease, including PH as the result of chronic heart, lung, and systemic conditions. Over the past several decades, even the classic idiopathic (previously primary) PAH description has evolved as we have come to understand epidemiology in the modern treatment era. In all forms, PH and PAH cause significant morbidity and mortality from progressive right heart failure. A number of observational studies are now available, spanning PH population-based cohorts and PAH center-based registries. Reviewing the epidemiology of all subtypes of PH may elucidate commonalities along the spectrum of pulmonary vascular disease and identify critical areas for future study.

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Authors and Affiliations

  1. Division of Cardiology, Department of Medicine, Providence VA Medical Center, Alpert Medical School of Brown University, 830 Chalkstone Ave, Providence, RI, 02908, USA

    Gaurav Choudhary MD

  2. Division of Pulmonary, Critical Care and Sleep Medicine, Departments of Medicine and Health Services Policy and Practice, Rhode Island Hospital, Alpert Medical School of Brown University, 593 Eddy Street, Providence, RI, 02903, USA

    Corey E. Ventetuolo MD, MS

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  1. Gaurav Choudhary MD
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Correspondence to Gaurav Choudhary MD .

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Editors and Affiliations

  1. Cardiovascular Medicine Dept, Harvard Medical School Brigham and Women’s Hospital, Boston, Massachusetts, USA

    Bradley A. Maron

  2. Pulmonary & Critical Care Medicine, Stanford University Medical Center, Stanford, California, USA

    Roham T. Zamanian

  3. Pulmonary Critical Care Medicine Dept Cardiovascular Medicine Dept, Brigham and Women's Hospital Harvard Medical School, Boston, Massachusetts, USA

    Aaron B. Waxman

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Choudhary, G., Ventetuolo, C.E. (2016). Epidemiology of Pulmonary Hypertension: From Quaternary Referral Centre to the Community. In: Maron, B., Zamanian, R., Waxman, A. (eds) Pulmonary Hypertension. Springer, Cham. https://doi.org/10.1007/978-3-319-23594-3_4

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  • DOI: https://doi.org/10.1007/978-3-319-23594-3_4

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