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Nutrition in Infancy

  • Chapter
Nutrition in Cystic Fibrosis

Part of the book series: Nutrition and Health ((NH))

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Abstract

Nutritional deficiencies are usually the earliest manifestations in the infant with cystic fibrosis of whom about 85 % are pancreatic insufficient. Left untreated or undertreated PI will lead to chronic malnutrition. Due to the rapid growth and high metabolic demands in the first year, infants are at the highest risk of nutritional deficiencies if regular assessments and appropriate interventions are not implemented. Nutritional status is associated with progression of pulmonary disease as well as survival in CF; and therefore, early detection of nutritional deficiency and appropriate intervention is paramount to the health of the CF patient.

Upon diagnosis with CF, the goals are to attain and maintain normal growth and development. Long-term care is aimed at delaying progression of pulmonary disease through early detection and aggressive treatment of complications to prevent deterioration in lung function.

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Authors and Affiliations

  1. Section of Pediatric Pulmonology, Allergy, and Sleep Medicine, Indiana University Health, 705 Riley Hospital Drive/ROC 4270, Indianapolis, IN, 46202, USA

    Evans Machogu M.B.Ch.B., M.S.

  2. Cystic Fibrosis Program, Children’s Hospital of Wisconsin, 9000 W. Wisconsin Ave., Milwaukee, WI, 53201, USA

    Tami Miller R.D., C.S.P., C.D.

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  1. Evans Machogu M.B.Ch.B., M.S.
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  2. Tami Miller R.D., C.S.P., C.D.
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Correspondence to Tami Miller R.D., C.S.P., C.D. .

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Editors and Affiliations

  1. Department of Pediatrics, Division of Gastroenterology, Hepatology and Nutrition, University of California, San Francisco, San Francisco, California, USA

    Elizabeth H. Yen

  2. Gastorenterology and Nutrition, The Johns Hopkins Children’s Center, Baltimore, Maryland, USA

    Amanda Radmer Leonard

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Machogu, E., Miller, T. (2015). Nutrition in Infancy. In: Yen, E., Leonard, A. (eds) Nutrition in Cystic Fibrosis. Nutrition and Health. Humana Press, Cham. https://doi.org/10.1007/978-3-319-16387-1_6

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  • DOI: https://doi.org/10.1007/978-3-319-16387-1_6

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