Abstract
Considering the significant limitations of basic echocardiography in the evaluation of arrhythmogenic right ventricular cardiomyopathy (ARVC), substantial research has been made in recent years regarding the possible diagnostic contribution of advanced echocardiographic techniques in this disease. Three-dimensional echocardiography has good accuracy for RV volumes and ejection fraction assessment with respect to cardiac magnetic resonance in ARVC patients. Furthermore, tissue Doppler imaging allows quantitative assessment of RV longitudinal function by measuring myocardial velocities and velocity-derived deformation parameters (strain and strain rate) and provides interesting information in ARVC patients, considering the dyshomogeneous nature of myocardial involvement in this peculiar type of cardiomyopathy. Finally, speckle-tracking echocardiography applied in ARVC shows significantly reduced RV global longitudinal strain in this patient population.
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Dragos, A.M., Abate, E., Pinamonti, B. (2014). Advanced Echocardiographic Techniques in Arrhythmogenic Right Ventricular Cardiomyopathy. In: Pinamonti, B., Sinagra, G. (eds) Clinical Echocardiography and Other Imaging Techniques in Cardiomyopathies. Springer, Cham. https://doi.org/10.1007/978-3-319-06019-4_16
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DOI: https://doi.org/10.1007/978-3-319-06019-4_16
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