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Adult Congenital Heart Disease

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Cardiac Surgery Clerkship

Part of the book series: Contemporary Surgical Clerkships ((CSC))

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Abstract

With advances in surgical techniques and medical therapies, survival rates of congenital heart disease have improved dramatically, with 90% of patients surviving into adulthood (Menachem et al., JACC Heart Fail 8(2):87–99, 2020, Brida and Gatzoulis, Acta Paediatr 108(10):1757–64, 2019). As a result, adults with congenital heart disease (ACHD) represent one of the fastest growing populations in need of cardiac surgery, thus the understanding of ACHD becomes an important skill for the contemporary cardiac surgeon. Summarized here are the most common ACHD presentations, key clinical factors and anatomic considerations, and current surgical management.

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References

  1. Brida M, Gatzoulis MA. Adult congenital heart disease: past, present and future. Acta Paediatr. 2019;108(10):1757–64. https://doi.org/10.1111/apa.14921.

    Article  PubMed  Google Scholar 

  2. Angelini A, di Gioia C, Doran H, Fedrigo M, Henriques de Gouveia R, Ho SY, et al. Autopsy in adults with congenital heart disease (ACHD). Virchows Arch. 2020;476(6):797–820. https://doi.org/10.1007/s00428-020-02779-8.

    Article  CAS  PubMed  PubMed Central  Google Scholar 

  3. Pendela VS, Tan BE, Chowdhury M, Chow M. Partial anomalous pulmonary venous return presenting in adults: a case series with review of literature. Cureus. 2020;12(6):e8388. https://doi.org/10.7759/cureus.8388.

    Article  PubMed  PubMed Central  Google Scholar 

  4. Kastellanos S, Aznaouridis K, Vlachopoulos C, Tsiamis E, Oikonomou E, Tousoulis D. Overview of coronary artery variants, aberrations and anomalies. World J Cardiol. 2018;10(10):127–40. https://doi.org/10.4330/wjc.v10.i10.127.

    Article  PubMed  PubMed Central  Google Scholar 

  5. Ansari MM, Cardoso R, Garcia D, Sandhu S, Horlick E, Brinster D, et al. Percutaneous pulmonary valve implantation: present status and evolving future. J Am Coll Cardiol. 2015;66(20):2246–55. https://doi.org/10.1016/j.jacc.2015.09.055.

    Article  PubMed  Google Scholar 

  6. Blissett S, Lin S, Mahadevan V, Ordovas K. Adult presentation of congenital heart disease. Semin Roentgenol. 2020;55(3):251–63. https://doi.org/10.1053/j.ro.2020.06.008.

    Article  PubMed  Google Scholar 

  7. Zimmerman SL. Intramural versus septal course for anomalous interarterial coronary arteries. In: Earls and pitfalls in cardiovascular imaging: pseudolesions, artifacts and other difficult diagnoses. Cambridge: Cambridge University Press; 2015. p. 113–6.

    Chapter  Google Scholar 

  8. Krasuski RA, Magyar D, Hart S, Kalahasti V, Lorber R, Hobbs R, et al. Long-term outcome and impact of surgery on adults with coronary arteries originating from the opposite coronary cusp. Circulation. 2011;123(2):154–62. https://doi.org/10.1161/CIRCULATIONAHA.109.921106.

    Article  PubMed  Google Scholar 

  9. Mascio CE, Austin EH. Vascular rings, slings, and other arch anomalies. 2016. https://thoracickey.com/vascular-rings-slings-and-other-arch-anomalies/. Accessed 7 Apr 2022.

  10. Liberthson RR, Pennington DG, Jacobs ML, Daggett WM. Coarctation of the aorta: review of 234 patients and clarification of management problems. Am J Cardiol. 1979;43(4):835–40. https://doi.org/10.1016/0002-9149(79)90086-9.

    Article  CAS  PubMed  Google Scholar 

  11. Alkashkari W, Albugami S, Hijazi ZM. Management of coarctation of the aorta in adult patients: state of the art. Korean Circ J. 2019;49(4):298–313. https://doi.org/10.4070/kcj.2018.0433.

    Article  PubMed  PubMed Central  Google Scholar 

  12. Jha AK, Makhija N. Cor triatriatum: a review. Semin Cardiothorac Vasc Anesth. 2017;21(2):178–85. https://doi.org/10.1177/1089253216680495.

    Article  PubMed  Google Scholar 

  13. Hussain ST, Mawulawde K, Stewart RD, Pettersson GB. Cor triatriatum dexter: a rare cause of myocardial infarction and pulmonary embolism in a young adult. J Thorac Cardiovasc Surg. 2015;149(3):e48–50. https://doi.org/10.1016/j.jtcvs.2014.11.078.

    Article  PubMed  Google Scholar 

  14. Rao PS. Single ventricle—a comprehensive review. Children (Basel). 2021;8(6):441. https://doi.org/10.3390/children8060441.

    Article  PubMed  PubMed Central  Google Scholar 

  15. Geoffrion T, Fuller S. Surgery for adult congenital heart disease. Cardiol Clin. 2020;38(3):435–43. https://doi.org/10.1016/j.ccl.2020.04.013.

    Article  PubMed  Google Scholar 

  16. Menachem JN, Schlendorf KH, Mazurek JA, Bichell DP, Brinkley DM, Frischhertz BP, et al. Advanced heart failure in adults with congenital heart disease. JACC Heart Fail. 2020;8(2):87–99. https://doi.org/10.1016/j.jchf.2019.08.012.

    Article  PubMed  Google Scholar 

  17. Dipchand AI, Honjo O, Alonso-Gonzalez R, McDonald M, Roche SL. Heart transplant indications, considerations and outcomes in Fontan patients: age-related nuances, transplant listing and disease-specific indications. Can J Cardiol. 2022;38(7):1072–85. https://doi.org/10.1016/j.cjca.2022.02.019.

    Article  PubMed  Google Scholar 

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Authors and Affiliations

  1. Division of Cardiac Surgery, Massachusetts General Hospital, Boston, MA, USA

    Selena S. Li & Jordan P. Bloom

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  1. Selena S. Li
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  2. Jordan P. Bloom
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Correspondence to Jordan P. Bloom .

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Editors and Affiliations

  1. Cardiac Surgery, Massachusetts General Hospital, Boston, MA, USA

    Jordan P. Bloom

  2. Cardiac Surgery, Mass General Hospital, Boston, MA, USA

    Thoralf M. Sundt

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© 2024 The Author(s), under exclusive license to Springer Nature Switzerland AG

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Li, S.S., Bloom, J.P. (2024). Adult Congenital Heart Disease. In: Bloom, J.P., Sundt, T.M. (eds) Cardiac Surgery Clerkship. Contemporary Surgical Clerkships. Springer, Cham. https://doi.org/10.1007/978-3-031-41301-8_33

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  • DOI: https://doi.org/10.1007/978-3-031-41301-8_33

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  • Publisher Name: Springer, Cham

  • Print ISBN: 978-3-031-41300-1

  • Online ISBN: 978-3-031-41301-8

  • eBook Packages: MedicineMedicine (R0)

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