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Primary Ciliary Dyskinesia

Clinical Features and Management of Disease

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Airway diseases

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Abstract

Primary ciliary dyskinesia (PCD) is a rare disease characterized by abnormal ciliary function due to defects in the structure and/or function of motile cilia. As the motile cilia are found on the epithelial surface of the upper and lower respiratory tract and middle ear and as they have a critical role in the local defense of the airways, dysfunction of motile cilia leads to impaired mucociliary clearance resulting in recurrent and chronic infections of the upper and lower airways [1].

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Authors and Affiliations

  1. Division of Pediatric Pulmonology, Department of Pediatrics, Faculty of Medicine, Medipol University, İstanbul, Turkey

    Emine Atağ & Yasemin Gökdemir

  2. Department of General Pediatrics, University Hospital Muenster, Muenster, Germany

    Heymut Omran

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  1. Emine Atağ
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  2. Yasemin Gökdemir
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  3. Heymut Omran
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Correspondence to Emine Atağ .

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Editors and Affiliations

  1. Department of Otorhinolaryngology, Eskişehir Osmangazi University, Eskisehir, Türkiye

    Cemal Cingi

  2. Department of Pulmonology, Celal Bayar University, Manisa, Türkiye

    Arzu Yorgancıoğlu

  3. Department of Otorhinolaryngology, Kırıkkale University, Kırıkkale, Türkiye

    Nuray Bayar Muluk

  4. Federal University of Bahia School of Medicine and ProAR Foundation, Salvador - Bahia, Brazil

    Alvaro A. Cruz

Section Editor information

  1. Pediatric Pulmonology, Marmara University Faculty of Medicine, Istanbul, Türkiye

    Bulent Karadag

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Atağ, E., Gökdemir, Y., Omran, H. (2023). Primary Ciliary Dyskinesia. In: Cingi, C., Yorgancıoğlu, A., Bayar Muluk, N., Cruz, A.A. (eds) Airway diseases. Springer, Cham. https://doi.org/10.1007/978-3-031-22483-6_105-1

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