Abstract
Prader-Willi syndrome (PWS) is a is a pervasive neurodevelopmental syndrome with a characteristic behavior profile that includes a typical yet abnormal food-related behavior profile as well as a more general behavior phenotype that includes a risk for behavior disorders and, for some, psychiatric problems. To date, most research has focused on identifying and describing the dimensions of the abnormal food-related behavior constellation and the more general behavior phenotype and the impact of genetic subtype on those behaviors. Effective behavior management strategies have received less attention. This chapter will first detail typical behavioral characteristics associated with PWS across the life span, will examine critical management issues, and finally will provide strategies for effective management. In addition to general principles, an extensive table of typical behaviors both at home and at school provides specific management tips and techniques found to be effective. This table can be copied and posted for quick reference.
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Whitman, B.Y., Graziano, L.A. (2022). Tools for Psychological and Behavioral Management with Prader-Willi Syndrome. In: Butler, M.G., Lee, P.D.K., Whitman, B.Y. (eds) Management of Prader-Willi Syndrome. Springer, Cham. https://doi.org/10.1007/978-3-030-98171-6_12
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