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Rare Sinonasal and Skull Base Tumors

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Sinonasal and Skull Base Malignancies

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Abstract

The sinonasal and skull base regions give rise to a diverse range of benign and malignant neoplasms, many of which are remarkably rare. This diversity in part makes sinonasal tract pathology one of the more challenging areas of head and neck surgical pathology. Not uncommonly, ancillary testing is required to distinguish a suspected diagnosis from its mimickers, highlighting the importance of generous biopsy material. The most recent WHO classification of head and neck tumors has more fully characterized a number of sinonasal neoplasms in comparison to prior editions due to advances in understanding of their underlying genetic mechanisms. This chapter focuses on rare sinonasal and skull base neoplasms, with an emphasis on pertinent diagnostic morphologic features and attention to ancillary testing.

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Authors and Affiliations

  1. Department of Pathology and Laboratory Medicine, Emory University, Atlanta, GA, USA

    Kelly R. Magliocca

  2. Robert J. Tomsich Pathology and Laboratory Medicine Institute Department of Pathology, Cleveland Clinic Foundation, Cleveland, OH, USA

    Christopher C. Griffith

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  1. Department of Hematology and Medical Oncology, Emory University School of Medicine, Atlanta, GA, USA

    Nabil F. Saba

  2. Department of Otolaryngology, Harvard University, Boston, MA, USA

    Derrick T. Lin

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Magliocca, K.R., Griffith, C.C. (2022). Rare Sinonasal and Skull Base Tumors. In: Saba, N.F., Lin, D.T. (eds) Sinonasal and Skull Base Malignancies. Springer, Cham. https://doi.org/10.1007/978-3-030-97618-7_12

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